ORPHA:622014
Autoimmune encephalitis
Synonyms: AE · AIE
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
10 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Autoimmune encephalitis | AE · AIE |
| fr | Encéphalite auto-immune | EA · EAI |
| de | Enzephalitis, autoimmune | AIE · Autoimmun-Enzephalitis |
| es | Encefalitis autoinmune | EA · EAI |
| it | Encefalite autoimmune | = en |
| nl | Auto-immune encefalitis | = en |
| pt | Encefalite autoimune | = en |
| pl | Autoimmunologiczne zapalenie mózgu | = en |
| cs | Autoimunitní encefalitida | = en |
| uk | Аутоімунний енцефаліт | = en |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0020640 | E | validated | |
| UMLS | C5671289 | E | validated | |
| GARD | 11979 | E | validated | |
| MedDRA | 10072378 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:97275Encephalitis
rare neurological diseases
Children (11):
- ORPHA:83597Acute disseminated encephalomyelitis
- ORPHA:623615Autoimmune limbic encephalitis
- ORPHA:79138Bickerstaff brainstem encephalitis
- ORPHA:623638Immune-mediated cerebellar ataxia
- ORPHA:217253NMDA receptor encephalitis
- ORPHA:624199Non-specific autoimmune brainstem encephalitis with characteristic antibodies
- ORPHA:624216Non-specific autoimmune brainstem encephalitis without characteristic antibodies
- ORPHA:624166Non-specific autoimmune supratentorial encephalitis with characteristic antibodies
- ORPHA:624178Non-specific autoimmune supratentorial encephalitis without characteristic antibodies
- ORPHA:624190Paraneoplastic isolated brainstem encephalitis
- ORPHA:83601Steroid-responsive encephalopathy associated with autoimmune thyroiditis
Codes that Orphanet moved or referred to this one:
- ORPHA:98253OBSOLETE: Postinfectious encephalitis referred to · inactive
- ORPHA:163892OBSOLETE: Limbic encephalitis referred to · inactive
- ORPHA:163895OBSOLETE: Paraneoplastic limbic encephalitis referred to · inactive
- ORPHA:163898OBSOLETE: Classic paraneoplastic limbic encephalitis referred to · inactive
- ORPHA:163903OBSOLETE: Limbic encephalitis associated with antibodies to cell membrane antigens referred to · inactive
- ORPHA:163908OBSOLETE: Limbic encephalitis with LGI1 antibodies referred to · inactive
- ORPHA:163914OBSOLETE: Limbic encephalitis with nCMAgs antibodies referred to · inactive
- ORPHA:163918OBSOLETE: Non-paraneoplastic limbic encephalitis referred to · inactive
- ORPHA:163924OBSOLETE: Non-herpetic acute limbic encephalitis referred to · inactive
- ORPHA:276402OBSOLETE: Limbic encephalitis with caspr2 antibodies referred to · inactive
- ORPHA:329341OBSOLETE: Limbic encephalitis with DPP6 antibodies referred to · inactive
- ORPHA:498700OBSOLETE: Limbic encephalitis with neurexin-3 antibodies referred to · inactive
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/622014
- This record as JSON: /data/d/622014.json