ORPHA:60039
Pudendal nerve entrapment syndrome
Synonyms: Alcock syndrome · Pudendal algia · Pudendal neuralgia · Pudendal neuralgia by pudendal nerve entrapment · Pudendal neuropathic pain syndrome · Pudendal neuropathy · Pudendalgia
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare, acquired peripheral neuropathy characterized by chronic neuropathic pain involving the sensory territory of the pudendal nerve (from clitoris to anus or from penis to anus) aggravated by sitting. It is often associated with pelvic dysfunction.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Pudendal nerve entrapment syndrome | Alcock syndrome · Pudendal algia · Pudendal neuralgia · Pudendal neuralgia by pudendal nerve entrapment · Pudendal neuropathic pain syndrome · Pudendal neuropathy · Pudendalgia |
| fr | Syndrome de compression du nerf pudendal | Algie pudendale · Neuropathie pudendale · Névralgie par compression du nerf pudendal · Névralgie pudendale · Pudendalgie · Syndrome d'Alcock · Syndrome de douleur neuropathique pudendale |
| de | Pudendus-Nervenkompression | Pudendusneuralgie durch Einklemmung des Pudendusnervs · Pudendusneuropathie · Alcock-Syndrom · Neuropathisches Schmerzsyndrom des Pudendus · Pudendusneuralgie |
| es | Síndrome de atrapamiento del nervio pudendo | Algia pudenda · Neuralgia del pudendo · Neuralgia pudenda por atrapamiento del nervio pudendo · Neuropatía pudenda · Pudendalgia · Síndrome de Alcock · Síndrome de dolor neuropático pudendo |
| it | Sindrome da intrappolamento del nervo pudendo | Algia del pudendo · Neuropatia del pudendo · Nevralgia da intrappolamento del nervo pudendo · Nevralgia del pudendo · Pudendalgia · Sindrome da dolore neuropatico del pudendo · Sindrome di Alcock |
| nl | Nervus pudendus-entrapmentsyndroom | Beknelling van schaamzenuw-syndroom · Pudendale neuropathische pijn-syndroom · Pudendusneuralgie · Pudendusneuralgie door beknelling van nervus pudendus · Pudendusneuropathie · Syndroom van Alcock |
| pt | Síndrome de encarceramento do nervo pudendo | Algia do pudendo · Neuralgia do pudendo · Neuralgia do pudendo por encarceramento do nervo · Neuropatia do pudendo · Pudendalgia · Síndrome Alcock · Síndrome de dor neuropática do pudendo |
| pl | Neuralgia nerwu sromowego | Ból sromu · Zespół Alcocka · Zespół uwięźnięcia nerwu sromowego |
| cs | Pudendální neuralgie | Pudendální algie · Úžinový syndrom pudendálního nervu · Pudendalgie · Alcockův syndrom · Pudendální neuralgie způsobená kompresí pudendálního nervu |
| uk | Синдром защемлення малогомілкового нерва | Синдром Алькока · Пудендальська водорость · Невралгія корінцевого нерва · Пудендальна невралгія внаслідок защемлення сідничного нерва · Пудендальний невропатичний больовий синдром · Пудендальна нейропатія · Пудендальгія |
| zh | 阴部神经痛 | 阴部神经痛伴阴部神经压迫 |
| tr | Pudendal nevralji | Pudendalji · Pudendal alji · Alcock sendromu · Pudendal sinir sıkışması sendromu · Pudendal sinir sıkışmasına bağlı pudendal nevralji |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G58.8 | NTBT | attributed | validated |
| ICD-11 | GA34.0Y | NTBT | index | validated |
| MONDO | 0018957 | E | validated | |
| MeSH | D060545 | E | validated | |
| UMLS | C3178970 | E | validated | |
| GARD | 10713 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:182086Acquired peripheral neuropathy
rare neurological diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | 20071246[PMID] |
| Point prevalence | 1-5 / 10 000 | 16.67 / 100 000 | France | Value and class | Validated | [EXPERT] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
19 annotations · validated 2023-06-26| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0012533 | Allodynia | Diagnostic criterion |
| HP:0500005 | Anal pain | Diagnostic criterion |
| HP:0030016 | Dyspareunia | |
| HP:0100518 | Dysuria | |
| HP:0100639 | Erectile dysfunction | |
| HP:0033345 | Neuralgia | Diagnostic criterion |
| HP:0032150 | Paroxysmal rectal pain | Diagnostic criterion |
| HP:0100515 | Pollakisuria | |
| HP:0030155 | Scrotal pain | Diagnostic criterion |
| HP:0030943 | Vulvodynia | Diagnostic criterion |
| Frequent (79-30%) | ||
| HP:0034805 | Buttock pain | |
| HP:0034267 | Pelvic pain | |
| HP:0034806 | Vaginal foreign body sensation | Diagnostic criterion |
| Excluded (0%) | ||
| HP:0001311 | Abnormal nervous system electrophysiology | Diagnostic criterion |
| HP:0030439 | Anal canal adenocarcinoma | |
| HP:0010787 | Genital neoplasm | |
| HP:0007379 | Neoplasm of the genitourinary tract | |
| HP:0000989 | Pruritus | |
| HP:0003474 | Somatic sensory dysfunction | |
Run the differential on the 10 obligate / very frequent terms
Annotation source: 17828787[PMID]_22110274[PMID]_24716710[PMID]
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/60039
- This record as JSON: /data/d/60039.json