raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:596941

Incomplete septal cirrhosis

Synonyms: Incomplete septal fibrosis

Type
Histopathological subtype
Group
Subtype of disorder
Inheritance
Not applicable
Status
active

A histopathological form of portosinusoidal vascular disease characterized by the presence of incomplete, thin, perforated, or blind-ended septa, which intermittently delimit rudimentary nodules, although complete cirrhotic-type regenerative nodules are not seen. Isolated collagen bundles can also be observed within the parenchyma.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enIncomplete septal cirrhosisIncomplete septal fibrosis
frCirrhose septale incomplèteFibrose septale incomplète
deUnvollständige SeptumzirrhoseUnvollständige Septumfibrose
esCirrosis septal incompletaFibrosis septal incompleta
itCirrosi settale incompletaFibrosi settale incompleta
nlIncomplete septale cirroseIncomplete septale fibrose
ptCirrose septal incompletaFibrose septal incompleta
plNiekompletne włóknienie przegrodowe= en
csNeúplná septální cirhóza= en
ukНеповний цироз печінкиНеповний фіброз перегородки
zhIncomplete septal cirrhosis= en
trIncomplete septal cirrhosis= en

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10K74.6NTBTattributedvalidated
MONDO0035696Evalidated
UMLSC0544815Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card