raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:592894

Acute disseminated encephalomyelitis with anti-MOG antibodies

Synonyms: ADEM with anti-MOG antibodies · Acute disseminated encephalomyelitis with anti-myelin oligodendrocyte glycoprotein antibodies

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Status
active

Orphadata ships no English definition for this code.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enAcute disseminated encephalomyelitis with anti-MOG antibodiesADEM with anti-MOG antibodies · Acute disseminated encephalomyelitis with anti-myelin oligodendrocyte glycoprotein antibodies
frEncéphalomyélite aiguë disséminée avec anticorps anti-MOGADEM avec anticorps anti-MOG
deAkute disseminierte Enzephalomyelitis mit anti-MOG-AntikörperADEM mit anti-MOG-Antikörper · Enzephalomyelitis, akute disseminierte, mit anti-Myelin-Oligodendrozyten-Glykoprotein-Antikörper
esEncefalomielitis diseminada aguda con anticuerpos anti-MOGEAD con anticuerpos anti-MOG · Encefalomielitis diseminada aguda con anticuerpos anti-glicoproteína mielínica oligodendrocitaria
itEncefalomielite acuta disseminata con anticorpi anti-MOGADEM con anticorpi anti-MOG · Encefalomielite acuta disseminata con anticorpi anti-glicoproteina mielinica oligodendrocitaria
nlAcute gedissemineerde encefalomyelitis met anti-MOG antilichamenADEM met anti-MOG antilichamen · Acute gedissemineerde encefalomyelitis met anti-myeline oligodendrocyt glycoproteïne antilichamen
ptEncefalomielite disseminada aguda com anticorpos anti-MOGADEM com anticorpos anti-MOG · Encefalomielite disseminada aguda com anticorpos anti-mielina glicoproteína oligodendrócitos
plOstre rozsiane zapalenie mózgu i rdzenia z przeciwciałami przeciw glikoproteinie oligodendrocytów mielinyOstre rozsiane zapalenie mózgu i rdzenia z przeciwciałami przeciw MOG
csAkutní diseminovaná encefalomyelitida s anti-MOG protilátkami= en
ukГострий дисемінований енцефаломієліт з антитілами до MOGГострий дисемінований енцефаломієліт з антитілами до глікопротеїну олігодендроцитів проти мієліну · ADEM з антитілами проти MOG
zhAcute disseminated encephalomyelitis with anti-MOG antibodies= en
trAcute disseminated encephalomyelitis with anti-MOG antibodies= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10G04.0NTBTspecificvalidated
MONDO0035669Evalidated
UMLSC5680301Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card