Isolated splenic vein thrombosis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare gastroenterologic disease characterized by isolated thrombotic obstruction of the splenic vein, typically due to pancreatic disorders, in particular acute or chronic pancreatitis or pancreatic neoplasms. It is the main cause of left-sided portal hypertension. Patients may be asymptomatic or present with abdominal pain, gastrointestinal bleeding, nausea, and vomiting, as well as signs of portal hypertension.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Isolated splenic vein thrombosis | |
| fr | Thrombose isolée de la veine splénique | |
| de | Milzvenenthrombose, isolierte | |
| es | Trombosis de la vena esplénica aislada | Trombosis venosa esplénica aislada |
| it | Trombosi isolata della vana splenica | |
| nl | Geïsoleerde trombose van vena splenica | Geïsoleerde trombose van miltader · Geïsoleerde trombose van vena lienalis |
| pt | Trombose isolada da veia esplénica | |
| pl | Izolowana zakrzepica żył śledzionowych | |
| cs | Izolovaná trombóza slezinné žíly | |
| uk | Ізольований тромбоз селезінкової вени | |
| zh | 孤立性脾静脉血栓 | |
| tr | İzole dalak ven trombozu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I82.8 | NTBT | attributed | validated |
| ICD-11 | DB98.4 | E | specific | validated |
| MONDO | 0035008 | E | validated | |
| UMLS | C0272416 | E | validated | |
| MedDRA | 10041659 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:97935Rare gastroenterologic disease
rare gastroenterological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/583856
- This record as JSON: /data/d/583856.json