raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:576360

Acquired human prion disease

Synonyms: Infectious human prion disease

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enAcquired human prion diseaseInfectious human prion disease
frMaladie à prion humaine acquiseMaladie à prion humaine infectieuse
dePrionkrankheit, humane, erworbene Form
esEnfermedad por priones humanos adquirida
itMalattia umana acquisita da prioniMalattia umana infettiva da prioni
nlVerworven humane prionziekte
ptDoença de priões humana adquirida
plNabyta ludzka choroba prionowa= en
csZískané lidské prionové onemocnění= en
ukНабута пріонна хвороба людиниІнфекційна пріонна хвороба людини
zh获得性人朊病毒病感染性人朊病毒病
trEdinsel insan prion hastalığıBulaşıcı insan prion hastalığı
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO0035562Evalidated
UMLSC5680357Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (2):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card