Anomalous aortic origin of the left coronary artery
Synonyms: AOLCA · L-ACAOS · Left coronary artery from right aortic sinus
- Type
- Morphological anomaly
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
A rare coronary artery congenital malformation characterized by an anomalous origin and course of the left coronary artery, which originates from the right aortic sinus of Valsalva and has an abnormal proximal course, which may be intramural, prepulmonic, subpulmonic, retroaortic, retrocardiac or wrapped around the apex. Patients are frequently asymptomatic, although chest pain, dyspnea, palpitations, dizziness, syncope, and sudden cardiac arrest/death (typically following intense physical exertion) may be observed. This malformation is associated with a high risk of sudden cardiac death so surgical revascularization is recommended even in cases with no associated evidence of myocardial ischemia.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Anomalous aortic origin of the left coronary artery | AOLCA · L-ACAOS · Left coronary artery from right aortic sinus |
| fr | Anomalie de naissance de l'artère coronaire gauche à partir de l'aorte | Anomalie d'origine de l'artère coronaire gauche à partir de l'aorte · L-ACAOS · Naissance de l'artère coronaire gauche à partir du sinus droit |
| de | Anomaler Abgang der linken Koronararterie | Fehlabgang der linken Koronararterie aus dem rechten Aortensinus |
| es | Origen anómalo de la arteria coronaria izquierda | AOLCA · Arteria coronaria izquierda en el seno aórtico derecho · L-ACAOS |
| it | Origine anomala dell'arteria coronaria sinistra dall'aorta | |
| nl | Aberrante oorsprong van linkerkransslagader in aorta | AOLCA · L-ACAOS · Linkerkransslagader uit rechter sinus van Valsalva |
| pt | Artéria coronária esquerda com origem aórtica anómala | |
| pl | Nieprawidłowe odejście lewej tętnicy wieńcowej od aorty | = en |
| cs | Anomální aortální odstup levé koronární tepny | AOLCA · L-ACAOS · Levá koronární tepna z pravého aortálního sinu |
| uk | Аномальне відходження лівої коронарної артерії від аорти | AOLCA · L-ACAOS · Ліва коронарна артерія від правого аортального синуса |
| zh | 主动脉起源性左冠状动脉起源异常 | 左冠状动脉起源于右主动脉窦 |
| tr | Sol koroner arterin anormal aort orijini | AOLCA · L-ACAOS · Sağ aort sinüsünden sol koroner arter |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | Q24.5 | NTBT | attributed | validated |
| ICD-11 | LA8C.1 | NTBT | index | validated |
| MONDO | 0035249 | E | validated | |
| UMLS | C3532026 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:541478Anomalous aortic origin of coronary artery
rare developmental anomalies during embryogenesis; rare cardiac malformations
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/541443
- This record as JSON: /data/d/541443.json