Mooren ulcer
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Status
- active
A rare disorder of the anterior segment of the eye characterized by a unilateral or bilateral rapidly progressive, intractable, painful, ulcerative keratitis which initially affects the peripheral cornea and may spread circumferentially and then centrally. The destructive process involves stromal corneal tissue only, leaving the epithelium and endothelium largely unaffected. There is no involvement of the adjacent sclera. The condition can be complicated by glaucoma, cataract, and perforation.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Mooren ulcer | |
| fr | Ulcère de Mooren | |
| de | Ulcus Mooren | Mooren-Ulkus |
| es | Úlcera de Mooren | |
| it | Ulcera di Mooren | |
| nl | Ulcus van Mooren | |
| pt | Úlcera Mooren | |
| pl | Wrzód Moorena | |
| cs | Moorenův vřed | |
| uk | Виразка Мурена | |
| zh | 蚕食性角膜溃疡 | |
| tr | Mooren ülseri |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | H16.0 | NTBT | inclusion | validated |
| ICD-11 | 9A76 | NTBT | index | validated |
| MONDO | 0001032 | E | validated | |
| UMLS | C0155072 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:519288Rare disorder with corneal involvement as a major feature
rare ophthalmic disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/519408
- This record as JSON: /data/d/519408.json