Non-functioning neuroendocrine tumor of pancreas
Synonyms: Non-functioning PNET · Non-functioning pancreatic NET · Non-functioning pancreatic neuroendocrine tumor · Non-functioning well-differentiated NEN of pancreas · Non-functioning well-differentiated neuroendocrine neoplasm of pancreas · Non-functioning well-differentiated pancreatic NEN · Non-functioning well-differentiated pancreatic neuroendocrine neoplasm
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare neuroendocrine tumor of pancreas characterized by a well-differentiated epithelial pancreatic neuroendocrine neoplasm measuring at least 0.5 cm, without distinct hormonal syndrome. Tumors <0.5 cm are called microadenomas. Microadenomatosis is the multifocal occurrence of microadenomas. Histopathologic examination shows an organoid growth pattern and expression of synaptophysin and chromogranin A on immunohistochemistry. Tumors are often discovered incidentally, or patients may present with symptoms related to local or metastatic tumor spread. Microadenomas are considered benign, while larger tumors may behave in a malignant manner with extrapancreatic spread, metastasis, or recurrence.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Non-functioning neuroendocrine tumor of pancreas | Non-functioning PNET · Non-functioning pancreatic NET · Non-functioning pancreatic neuroendocrine tumor · Non-functioning well-differentiated NEN of pancreas · Non-functioning well-differentiated neuroendocrine neoplasm of pancreas · Non-functioning well-differentiated pancreatic NEN · Non-functioning well-differentiated pancreatic neuroendocrine neoplasm |
| fr | Tumeur neuroendocrine non fonctionnelle du pancréas | NEN du pancréas bien différencié non fonctionnel · NEN pancréatique bien différencié non fonctionnel · Néoplasme neuroendocrine du pancréas bien différencié non fonctionnel · Néoplasme neuroendocrine pancréatique bien différencié non fonctionnel · PNET non fonctionnelle |
| de | Nicht-funktioneller neuroendokriner Tumor des Pankreas | Nicht-funktionelle hoch-differenzierte neuroendokrine Neoplasie des Pankreas · Nicht-funktioneller PNET · Nicht-funktioneller hoch-differenzierter NET des Pankreas |
| es | Tumor neuroendocrino de páncreas no funcionante | NEN de páncreas no funcionante bien diferenciada · NEN pancreática no funcionante bien diferenciada · Neoplasia neuroendocrina de páncreas no funcionante bien diferenciada · Neoplasia neuroendocrina pancreática no funcionante bien diferenciada · TNE pancreático no funcionante · TNEP no funcionante · Tumor neuroendocrino pancreático no funcionante |
| it | Tumore neuroendocrino pancreatico non funzionante | |
| nl | Niet-functionele neuro-endocriene tumor van pancreas | Niet-functioneel goed gedifferentieerd NEN van pancreas · Niet-functioneel goed gedifferentieerd neuro-endocrien neoplasma van pancreas · Niet-functioneel goed gedifferentieerd pancreatisch NEN · Niet-functioneel goed gedifferentieerd pancreatisch neuro-endocrien neoplasma · Niet-functionele PNET · Niet-functionele neuro-endocriene tumor van alvleesklier · Niet-functionele pancreatische NET · Niet-functionele pancreatische neuro-endocriene tumor |
| pt | Tumor neuroendócrino não-funcionante do pâncreas | |
| pl | Rak neuroendokrynny trzustki nieczynny hormonalnie | Rak trzustki nieczynny neuroendokrynnie |
| cs | Nefunkční neuroendokrinní tumor pankreatu | Nefunkční PNET · Nefunkční pankreatický NET · Nefunkční pankreatický neuroendokrinní tumor · Nefunkční dobře diferencovaný pankreatický NEN · Nefunkční dobře diferencovaný NEN pankreatu · Nefunkční dobře diferencovaný pankreatický neuroendokrinní novotvar · Nefunkční dobře diferencovaný neuroendokrinní novotvar pankreatu |
| uk | Нефункціонуюча нейроендокринна пухлина підшлункової залози | Нефункціонуюча панкреатична NEТ · Нефункціонуюча нейроендокринна пухлина підшлункової залози · Непрацююча PNEТ · Нефункціонуючий добре диференційований NEN підшлункової залози · Нефункціонуюча добре диференційована нейроендокринна пухлина підшлункової залози · Нефункціонуючий добре диференційований панкреатичний NEN · Нефункціонуюча добре диференційована нейроендокринна пухлина підшлункової залози |
| zh | 非功能性胰腺神经内分泌肿瘤 | 非功能性高分化胰腺神经内分泌肿瘤 |
| tr | Pankreas fonksiyonel olmayan nöroendokrin tümörü | Fonksiyonel olmayan PNET · Fonksiyonel olmayan PankreastikNET · Fonksiyonel olmayan pankreatik nöroendokrin tümörü · Fonksiyonel olmayan iyi ayırt edilmiş pankreatik NEN · Pankreasın fonksiyonel olmayan iyi ayırt edilmiş NEN'i · Fonksiyonel olmayan iyi ayırt edilmiş pankreatik nöroendokrin neoplazmı · Fonksiyonel olmayan iyi ayırt edilmiş pankreasın nöroendokrin neoplazmı |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C25.4 | NTBT | attributed | validated |
| ICD-11 | 2C10.1 | NTBT | attributed | validated |
| MONDO | 0004334 | E | validated | |
| MeSH | C536126 | E | validated | |
| UMLS | C1334977 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:97253Neuroendocrine tumor of pancreas
rare gastroenterological diseases; rare endocrine diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/506075
- This record as JSON: /data/d/506075.json