Phyllodes tumor of the prostate
Synonyms: Cystic epithelial-stromal tumors of the prostate · Cystosarcoma phyllodes of the prostate · Phyllodes type of atypical prostatic hyperplasia
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare urogenital tumor characterized by stromal and epithelial components forming cysts lined by hyperplastic epithelium in a cellular or sarcomatoid stroma. The tumors may be clinically benign or malignant and tend to recur after transurethral resection. Metastatic spread is to lungs, bone, and liver. Patients may present with obstructive voiding symptoms, dysuria, hematuria, urinary retention, or a palpable abdominal mass. The prostate is palpably enlarged but feels soft and spongy.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Phyllodes tumor of the prostate | Cystic epithelial-stromal tumors of the prostate · Cystosarcoma phyllodes of the prostate · Phyllodes type of atypical prostatic hyperplasia |
| fr | Tumeur phyllode de la prostate | Cystosarcome phyllode de la prostate · Cystosarcome phylloïde de la prostate · Tumeur phylloïde de la prostate |
| de | Phylloidtumor der Prostata | Cystosarcoma phyllodes der Prostata |
| es | Tumor filoides de la próstata | Cistosarcoma filoides de la próstata |
| it | Tumore filloide della prostata | |
| nl | Phyllodestumor van prostaat | Atypische hyperplasie van prostaat, phyllodes-type · Cystische epitheliale-stromale tumoren van prostaat · Cystosarcoma phyllodes van prostaat |
| pt | Tumor filóide da próstata | |
| pl | Guz liściasty prostaty | = en |
| cs | Phyllodes tumor prostaty | = en |
| uk | Фіброзна пухлина передміхурової залози | Кістозні епітеліально-стромальні пухлини передміхурової залози · Фіброаденома передміхурової залози · Аденома передміхурової залози за типом Філлодеса |
| zh | 前列腺叶状肿瘤 | 叶状不典型前列腺增生 |
| tr | Prostatın filloid tümörü | Prostatın sistosarkom filodları · Prostatın kistik epitel-stromal tümörleri · Atipik prostat hiperplazisinin filloid tipi |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C61 | NTBT | attributed | validated |
| ICD-11 | 2C82.Y | NTBT | attributed | validated |
| MONDO | 0021102 | E | validated | |
| UMLS | C1335409 | E | validated | |
| GARD | 9404 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:98058Rare urinary tract tumor
rare urogenital diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Cases/families | 90 cases | Worldwide | Case(s) | Validated | 25210561[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/498228
- This record as JSON: /data/d/498228.json