Idiopathic spontaneous coronary artery dissection
Synonyms: Idiopathic SCAD
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare vascular disease characterized by idiopathic detachment of the layers of the walls of coronary arteries, creating a false lumen which limits the main coronary flow, leading to myocardial ischemia. Clinical manifestations include acute coronary syndromes, especially ST-segment elevation myocardial infarction (STEMI), syncope, cardiogenic shock, or sudden cardiac death. The condition typically affects young women.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Idiopathic spontaneous coronary artery dissection | Idiopathic SCAD |
| fr | Dissection spontanée idiopathique de l'artère coronaire | DSAC idiopathique |
| de | Spontane Koronararteriendissektion | Idiopathische SCAD |
| es | Disección coronaria espontánea idiopática | DCE idiopática · Disección espontánea de arterias coronarias idiopática |
| it | Dissezione spontanea idiopatica dell'arteria coronaria | |
| nl | Idiopathische spontane dissectie van kransslagaders | Idiopathische SCAD |
| pt | Disseção espontânea idiopática da artéria coronária | |
| pl | Idiopatyczne spontaniczne rozwarstwienie tętnicy wieńcowej | Idiopatyczne SCAD |
| cs | Idiopatická spontánní disekce koronární artérie | Idiopatická SCAD |
| uk | Ідіопатичне спонтанне розшарування коронарних артерій | Ідіопатичний SCAD |
| zh | 特发性自发性冠状动脉夹层 | 特发性SCAD |
| tr | İdiyopatik spontan koroner arter diseksiyonu | İdiopatik SCAD |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| OMIM | 122455 | E | validated | |
| ICD-10 | I25.4 | NTBT | attributed | validated |
| ICD-11 | BA82 | NTBT | attributed | validated |
| MONDO | 0007385 | E | validated | |
| UMLS | C5679999 | E | validated | |
| GARD | 10822 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:97929Rare cardiac disease
rare cardiac diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Europe | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/458718
- This record as JSON: /data/d/458718.json