Endometrioid carcinoma of ovary
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult, Elderly
- Status
- active
A rare malignant epithelial tumor of ovary characterized by confluent or cribriform proliferations of round, oval, or tubular glands, typically lined by stratified non-mucin-containing epithelium with well-defined luminal margins. Squamous differentiation, secretory changes, oxyphilic variants, sex cord-stromal type patterns, or sertoliform endometrioid carcinomas may occur. Patients most commonly present in the sixth decade of life, either with a pelvic mass with or without pain, or without any symptoms. The tumor may be bilateral and is frequently associated with endometriosis and/or endometrial carcinoma.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Endometrioid carcinoma of ovary | |
| fr | Adénocarcinome endométrioïde de l'ovaire | |
| de | Endometrioides Ovarialkarzinom | Endometriumkarzinom des Ovars |
| es | Carcinoma endometrioide de ovario | |
| it | Carcinoma endometrioide dell'ovaio | |
| nl | Endometrioïd carcinoom van ovarium | |
| pt | Carcinoma endometrioide do ovário | |
| pl | Endometrialny rak jajnika | |
| cs | Endometroidní karcinom ovaria | |
| uk | Ендометріоїдна карцинома яєчника | |
| zh | 子宫内膜样卵巢癌 | |
| tr | Yumurtalıkta endometrioid karsinom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C56 | NTBT | attributed | validated |
| ICD-11 | 2C73.Y | NTBT | index | validated |
| MONDO | 0006335 | E | validated | |
| MONDO | 6335 | E | validated | |
| UMLS | C0346163 | E | validated | |
| MedDRA | 10073269 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:398934Malignant epithelial tumor of ovary
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 1 000 000 | 0.51 / 100 000 | Korea, Republic of | Value and class | Validated | 26463436[PMID] |
| Annual incidence | 1-9 / 1 000 000 | 0.81 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/454723
- This record as JSON: /data/d/454723.json