Incessant infant ventricular tachycardia
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Childhood, Infancy
- Status
- active
Incessant infant ventricular tachycardia is a rare type of ventricular tachycardia (VT) characterized by the presence of tachycardia originating from the ventricles, observed for more than 10% of a 24 hour monitoring period. Patients are either asymptomatic or present congestive heart failure.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Incessant infant ventricular tachycardia | |
| fr | Tachycardie ventriculaire incessante du nouveau-né | |
| de | Ventrikeltachykardie, anhaltende infantile | |
| es | Taquicardia ventricular incesante infantil | |
| it | Tachicardia ventricolare infantile continua | |
| nl | Aanhoudende infantiele ventrikeltachycardie | |
| pt | Taquicardia ventricular infantil persistente | |
| pl | Ustawiczny dziecięcy częstoskurcz komorowy | |
| cs | Incesantní kojenecká komorová tachykardie | |
| uk | Безперервна шлуночкова тахікардія у немовлят | |
| zh | 连续性婴儿室性心动过速 | |
| tr | Bebeğin sürekli ventrikül taşikardisi |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I47.2 | NTBT | attributed | validated |
| ICD-11 | BC71.0Y | NTBT | index | validated |
| MONDO | 0018685 | E | validated | |
| UMLS | C0340487 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:218439Non-genetic cardiac rhythm disease
rare cardiac diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
4 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Prevalence at birth | 1-9 / 100 000 | 1.5 / 100 000 | Europe | Value and class | Validated | [EXPERT] |
| Point prevalence | 1-9 / 100 000 | — | Europe | Class only | Validated | [EXPERT] |
| Prevalence at birth | 1-9 / 1 000 000 | 0.3 / 100 000 | United Kingdom | Value and class | Validated | 23551862[PMID] |
| Point prevalence | 1-9 / 1 000 000 | — | United Kingdom | Class only | Validated | 23551862[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
12 annotations · validated 2019-04-24| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Obligate (100%) | ||
| HP:0004756 | Ventricular tachycardia | Diagnostic criterion |
| Very frequent (99-80%) | ||
| HP:0031595 | Abnormal P wave | |
| HP:0011710 | Bundle branch block | |
| HP:0001695 | Cardiac arrest | |
| HP:0001635 | Congestive heart failure | |
| HP:0006677 | Prolonged QRS complex | |
| Frequent (79-30%) | ||
| HP:0009729 | Cardiac rhabdomyoma | |
| HP:0005152 | Histiocytoid cardiomyopathy | |
| HP:0001557 | Prenatal movement abnormality | |
| HP:0004755 | Supraventricular tachycardia | |
| Occasional (29-5%) | ||
| HP:0001716 | Wolff-Parkinson-White syndrome | |
| Excluded (0%) | ||
| HP:0025169 | Left ventricular systolic dysfunction | |
Run the differential on the 6 obligate / very frequent terms
Annotation source: 23438626[PMID]_18495675[PMID]_2387941[PMID]_3624668[PMID]
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/45453
- This record as JSON: /data/d/45453.json