raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:398053

Adenocarcinoma of the penis

Synonyms: Penile adenocarcinoma

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Elderly
Status
active

An extremely rare penile epithelial neoplasm, histologically composed of nests of epithelilal cells floating in lakes of extracellular, PAS-positive mucin, clinically characterized by a nonhealing ulcer or soft mass in the preputium or glans area, with itching and burning often preceding appearance of the lesion. Lymphadenopathy may indicate dissemination. Mucinous metaplasia of the penis may be a risk factor.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enAdenocarcinoma of the penisPenile adenocarcinoma
frAdénocarcinome de la vergeAdénocarcinome du pénis
deAdenokarzinom des Penis
esAdenocarcinoma del pene
itAdenocarcinoma del peneAdenocarcinoma penieno
nlAdenocarcinoom van penisPeniel adenocarcinoom
ptAdenocarcinoma do penisAdenocarcinoma peniano
plGruczolakorak penisaGruczolakorak prącia
csAdenokarcinom penisuPenilní adenokarcinom
ukАденокарцинома статевого членаАденокарцинома статевого члена
zh阴茎腺癌阴茎腺癌
trPenis adenokarsinomuPenil adenokarsinom

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C60.0NTBTattributedvalidated
ICD-10C60.1NTBTattributedvalidated
ICD-10C60.2NTBTattributedvalidated
ICD-10C60.8NTBTattributedvalidated
ICD-10C60.9NTBTattributedvalidated
ICD-112C81.YNTBTattributedvalidated
UMLSC2212153Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

17 records
TypeClassValueAreaQualificationValidationSource
Annual incidence<1 / 1 000 000—EuropeClass onlyValidated22119351[PMID]_RARECARE Surveillance of Rare Cancers in Europe 2003[OTHER]
Annual incidence<1 / 1 000 0000.006 / 100 000AustriaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.006 / 100 000BelgiumValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000BulgariaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000CroatiaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.004 / 100 000Czech RepublicValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.002 / 100 000FinlandValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.005 / 100 000GermanyValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000IrelandValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.004 / 100 000ItalyValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.005 / 100 000LatviaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.012 / 100 000LithuaniaValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.005 / 100 000NorwayValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.003 / 100 000PolandValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.025 / 100 000PortugalValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.004 / 100 000NetherlandsValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence<1 / 1 000 0000.006 / 100 000United KingdomValue and classValidatedRARECARE surveillance of rare cancers in Europe[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card