Serpiginous choroiditis
Synonyms: Geographic helicoid peripapillary choroidopathy
- Type
- Disease
- Group
- Disorder
- Status
- active
A rare non-infectious posterior uveitis characterized by usually bilateral, chronic, progressive, recurrent inflammation of the choroid, retinal pigment epithelium, and choriocapillaris. In the classic or peripapillary geographic type of the disease, infiltrates originating in the peripapillary region progress in an irregular serpentine fashion centrifugally and resolve spontaneously after several weeks, leaving atrophic scars. Multiple recurrences, often with months to years of quiescence in between, result in progressive visual loss in one or both eyes.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Serpiginous choroiditis | Geographic helicoid peripapillary choroidopathy |
| fr | Choroïdite serpigineuse | Choroïdopathie géographique hélicoïdale péripapillaire |
| de | Chorioditis, serpiginöse | Chorioidopathie, geografische helikoide peripapilläre |
| es | Coroiditis serpiginosa | Coroidopatía geográfica helicoidal peripapilar |
| it | Coroidite serpiginosa | Coroidopatia geografica elicoidale peripapillare |
| nl | Serpigineuze choroïditis | Geografische helicoïde peripapillaire choroïdopathie |
| pt | Coroidite em serpentina | Coroidopatia helicoidal peripapilar geográfica |
| pl | Choroidopatia pełzająca | = en |
| cs | Serpiginózní choroiditida | Geografická helikoidální peripapilární choroidopatie |
| uk | Серпігінозний хоріоїдит | Географічна гелікоїдна перипапілярна хоріодопатія |
| zh | 匐行性脉络膜炎 | 匐行性脉络膜萎缩 |
| tr | Serpijinöz koroidit | Coğrafi helikoid peripapiller koroidopati |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | H30.8 | NTBT | attributed | validated |
| ICD-11 | 9B65.0 | NTBT | index | validated |
| MONDO | 0018152 | E | validated | |
| UMLS | C0729842 | E | validated | |
| GARD | 31 | E | validated | |
| MedDRA | 10081652 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (3):
- ORPHA:90061Non-infectious posterior uveitis
rare ophthalmic disorders - ORPHA:716195Rare inflammatory choroidal disorder
rare ophthalmic disorders - ORPHA:716348Rare isolated progressive predominantly chorioretinal disorder
rare ophthalmic disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/35686
- This record as JSON: /data/d/35686.json