Quinquaud folliculitis decalvans
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A rare chronic inflammatory cicatricial alopecia of the scalp occurring in middle-aged adults and characterized by the development of alopecic patches with slowly centrifugal spread predominantly in the vertex and occipital area of the scalp, associated with perifollicular erythema, follicular pustules and hemorrhagic crusts.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Quinquaud folliculitis decalvans | |
| fr | Folliculite décalvante de Quinquaud | Folliculite épilante de Quinquaud |
| de | Folliculitis decalvans Quinquaud | |
| es | Foliculitis decalvante de Quinquaud | Foliculitis depilante de Quinquaud |
| it | Follicolite decalvante di Quinquaud | Follicolite depilante di Quinquaud |
| nl | Folliculitis decalvans van Quinquaud | |
| pt | Foliculite decalvante de Quinquaud | |
| pl | Wyłysiające zapalenie mieszków włosowych Quinquauda | |
| cs | Quinquaudova folliculitis decalvans | |
| uk | Епілюючий фолікуліт Квінке | |
| zh | Quinquaud脱发性毛囊炎 | |
| tr | Quinquaud foliküliti dekalvanları |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L66.2 | E | specific | validated |
| ICD-11 | ED70.50 | E | specific | validated |
| MONDO | 0018103 | E | validated | |
| UMLS | C2608043 | E | validated | |
| GARD | 373 | E | validated | |
| MedDRA | 10063921 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:79364Alopecia
rare skin diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
7 annotations · validated 2016-06-01| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0001595 | Abnormality of the hair | |
| HP:0010783 | Erythema | |
| HP:0002232 | Patchy alopecia | |
| HP:0200039 | Pustule | |
| HP:0001581 | Recurrent skin infections | |
| HP:0004552 | Scarring alopecia of scalp | |
| Frequent (79-30%) | ||
| HP:0100699 | Scarring | |
Run the differential on the 6 obligate / very frequent terms
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/346
- This record as JSON: /data/d/346.json