raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:3274

Granulomatous arthritis of childhood

inactive · moved to ORPHA:90340Blau syndrome

Synonyms: Autoinflammatory granulomatosis of childhood · Granulomatous inflammatory arthritis, dermatitis, and uveitis · Granulomatous synovitis-uveitis syndrome · PGA · Pediatric granulomatous arthritis

Type
Disease
Group
Disorder
Status
inactive
Flag
Deprecated entity

This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Blau syndrome

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enGranulomatous arthritis of childhoodAutoinflammatory granulomatosis of childhood · Granulomatous inflammatory arthritis, dermatitis, and uveitis · Granulomatous synovitis-uveitis syndrome · PGA · Pediatric granulomatous arthritis
frArthrite granulomateuse de l'enfantArthrite inflammatoire granulomateuse-dermatite-uvéite · Granulomatose auto-inflammatoire de l'enfant · PGA · Synovite granulomateuse-uvéite
deArthritis, granulomatöse des KindesaltersArthritis, granulomatöse inflammatorische - Dermatitis - Uveitis · Autoinflammatorische Granulomatose der Kindheit · PGA · Synovitis, granulomatöse - Uveitis
esArtritis granulomatosa de la infanciaAGP · Artritis granulomatosa pediátrica · Artritis inflamatoria granulomatosa, dermatitis y uveítis · Granulomatosis autoinflamatoria de la infancia · Sinovitis granulomatosa-uveítis
itArtrite granulomatosa dell'infanziaArtrite granulomatosa pediatrica · Artrite infiammatoria granulomatosa - dermatite - uveite · Granulomatosi autoinfiammatoria dell'infanzia · PGA · Sinovite granulomatosa - uveite
nlGranulomateuze artritis in de kinderjarenAuto-inflammatoire granulomatose in de kinderjaren · Granulomateuze inflammatoire artritis, dermatitis en uveïtis · Granulomateuze synovitis - uveïtis-syndroom · PGA · Pediatrische granulomateuze artritis
ptArtrite granulomatosa da infânciaArtrite granulomatosa pediátrica · Artrite inflamatória granulomatosa, dermatite e uveíte · Granulomatose autoinflamatória da infância · PGA · Síndrome de sinovite granulomatosa-uveíte
plDziecięce ziarniniakowe zapalenie stawówAutozapalenie ziarniniakowe wieku dzieciecego · Dziecięce ziarniniakowe zapalenie stawów · PGA · Ziarniniakowe zapalenie błony maziowej oraz błony naczyniowej · Ziarniniakowe zapalenie stawów, skóry i błony naczyniowej
csGranulomatózní artritida dětského věkuSyndrom zahrnující granulomatózní synovitidu a uveitidu · PGA · Zánětlivá granulomatóza dětského věku · Granulomatózní zánětlivá artritida, dermatitida a uveitida · Dětská granulomatózní artritida
ukГрануломатозний артрит дитячого вікуАутозапальний гранулематоз дитячого віку · Гранулематозний запальний артрит, дерматит та увеїт · Синдром гранулематозного синовіту-увеїту · Дитячий гранулематозний артрит · PGA
zh儿童肉芽肿性关节炎肉芽肿性炎症性关节炎,皮炎,葡萄膜炎
trÇocukluk çağı granülomatöz artritiPGA · Pediatrik granülomatöz artrit · Granülomatöz sinovit-üveit sendromu · Çocukluk çağının otoinflamatuvar granülomatozu · Granülomatöz iltihaplı artrit, dermatit ve üveit
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Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

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Sources for this card