Multilocular cystic renal neoplasm of low malignant potential
Synonyms: MCRCC · Multilocular clear cell adenocarcinoma · Multilocular clear cell carcinoma · Multilocular clear cell renal cell adenocarcinoma · Multilocular clear cell renal cell carcinoma · Multilocular cystic renal cell adenocarcinoma · Multilocular cystic renal cell carcinoma
- Type
- Histopathological subtype
- Group
- Subtype of disorder
- Status
- active
Multilocular cystic renal neoplasm of low malignant potential is a rare subtype of clear cell renal cell carcinoma with distinct pathological features of cysts lined by occasionally flattened cuboidal clear cells and septa containing aggregates of epithelial cells with clear cytoplasm, and excellent prognosis. The tumor usually presents as an asymptomatic, unilateral, solitary lesion, macroscopically consisting of numerous, fluid-filled, septated cysts of variable size. Rarely, the symptoms typically associated with renal tumors (flank pain, hematuria, palpable mass) may be present.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Multilocular cystic renal neoplasm of low malignant potential | MCRCC · Multilocular clear cell adenocarcinoma · Multilocular clear cell carcinoma · Multilocular clear cell renal cell adenocarcinoma · Multilocular clear cell renal cell carcinoma · Multilocular cystic renal cell adenocarcinoma · Multilocular cystic renal cell carcinoma |
| fr | Carcinome rénal kystique multiloculaire | Carcinome à cellules rénales kystique multiloculaire · MCRCC |
| de | Multilokuläre zystische Neoplasie der Niere von geringem malignen Potential | Adenokarzinom, klarzelliges multilokuläres · Karzinom, klarzelliges multilokuläres · MCRCC · Multilokuläres klarzelliges Adenokarzinom der Niere · Nierenzellkarzinom, klarzelliges multilokuläres · Nierenzellkarzinom, multilokuläres zystisches · Adenokarzinom der Niere, multilokuläres klarzelliges · Adenokarzinom der Niere, multilokuläres zystisches |
| es | Neoplasia renal quística multilocular de bajo potencial maligno | Adenocarcinoma multilocular de células claras · Adenocarcinoma renal multilocular de células claras · Carcinoma multilocular de células renales de células claras · Carcinoma quistico multilocular de células renales · MCRCC |
| it | Neoplasia renale cistica multiloculare a basso potenziale di malignità | |
| nl | Multiloculair cystisch neoplasma van nier met laag maligne potentieel | MCRCC · Multiloculair cystisch nierceladenocarcinoom · Multiloculair cystisch niercelcarcinoom · Multiloculair heldercellig adenocarcinoom · Multiloculair heldercellig carcinoom · Multiloculair heldercellig nierceladenocarcinoom · Multiloculair heldercellig niercelcarcinoom |
| pt | Carcinoma de células renais multilocular quístico | |
| pl | Wieloogniskowy torbielowaty jasnokomórkowy nowotwór nerki o niskim stopniu złośliwości | MCRCC · Wieloogniskowy torbielowaty rak z komórek nerkowych · Wieloogniskowy torbielowaty gruczolakorak z komórek nerkowych |
| cs | Multilokulární cystický karcinom ledviny | Multilokulární cystický renální adenokarcinom · Multilokulární adenokarcinom světlých buněk · Multilokulární karcinom světlých buněk · Multilokulární adenokarcinom světlých renálních buněk · Multilokulární karcinom světlých renálních buněk |
| uk | Мультилокулярна кістозна пухлина нирки з низьким злоякісним потенціалом | MCRCC · Мультилокулярна світлоклітинна аденокарцинома · Мультилокулярна світлоклітинна карцинома · Мультилокулярна прозороклітинна нирковоклітинна аденокарцинома · Мультилокулярна світлоклітинна нирковоклітинна карцинома · Мультилокулярна кістозна нирковоклітинна аденокарцинома · Мультилокулярна кістозна нирковоклітинна карцинома |
| zh | 低度恶性多囊肾肿瘤 | 多男性透明细胞腺癌 |
| tr | Düşük malignite potansiyeline sahip multiloküler kistik renal neoplazm | Multiloküler kistik renal hücreli karsinom · Multiloküler berrak hücreli renal hücreli karsinom · Multiloküler kistik renal hücreli adenokarsinom · Multiloküler berrak renal hücreli adenokarsinom · MCRCC · Multiloküler berrak hücreli karsinom · Multiloküler berrak hücreli adenokarsinom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C64 | NTBT | attributed | validated |
| MONDO | 0003010 | E | validated | |
| UMLS | C0346249 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:319276Clear cell renal carcinoma
rare renal diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/319287
- This record as JSON: /data/d/319287.json