Primary bone lymphoma
- Type
- Disease
- Group
- Disorder
- Age of onset
- All ages
- Status
- active
Primary bone lymphoma is a rare lymphoid hemopathy defined as single or multiple tumors in the bone, not associated with infringement or violation of other extranodal malignant lymph nodes outside the area. It usually presents with bone pain, nerve compression, a palpable mass or fracture, while systemic features (fever, night sweats, fatigue, loss of appetite, weight loss) are not common.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Primary bone lymphoma | |
| fr | Lymphome primitif des os | Lymphome osseux primitif |
| de | Knochenlymphom, primäres | |
| es | Linfoma óseo primario | |
| it | Linfoma primitivo dell'osso | |
| nl | Primair botlymfoom | |
| pt | Linfoma ósseo primário | |
| pl | Pierwotny chłoniak kości | |
| cs | Primární kostní lymfom | |
| uk | Первинна кісткова лімфома | |
| zh | 原发性骨淋巴瘤 | |
| tr | Primer kemik lenfoması |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C85.7 | NTBT | attributed | validated |
| MONDO | 0017814 | E | validated | |
| UMLS | C1332582 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:279911Primary organ-specific lymphoma
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/314684
- This record as JSON: /data/d/314684.json