raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:300849

Diffuse large B-cell lymphoma of the central nervous system

Synonyms: DLBCL of the CNS

Type
Disease
Group
Disorder
Inheritance
Multigenic/multifactorial, Not applicable
Status
active

This disease is described under Primary central nervous system lymphoma

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enDiffuse large B-cell lymphoma of the central nervous systemDLBCL of the CNS
frLymphome diffus à grandes cellules B du systéme nerveux centralDLBCL du CNS · DLBCL du SNC · Lymphome diffus à grandes cellules B du CNS · Lymphome diffus à grandes cellules B du SNC
deDiffuses großzelliges B-Zell-Lymphom des ZentralnervensystemsPrimäres DLBCL des Zentralnervensystems
esLinfoma difuso de células B grandes del sistema nervioso centralLDCBG del SNC
itLinfoma diffuso del sistema nervoso centrale a grandi cellule BDLBCL del SNC
nlDiffuus grootcellig B-cellymfoom van centraal zenuwstelselDLBCL van CZS
ptLinfoma difuso de células B grandes do sistema nervoso central
plChłoniak rozlany z dużych komórek B centralnego układu nerwowegoDLBCL CUN
csDifuzní velkobuněčný B-lymfom centrálního nervového systémuDLBCL CNS
ukДифузна велика В-клітинна лімфома центральної нервової системиDLBCL ЦНС
zh弥漫性中枢神经系统大B细胞淋巴瘤侵袭性B细胞非霍奇金淋巴瘤
trMerkezi sinir sisteminin diffüz büyük B-hücreli lenfomasıCNS'nin DLBCL'si
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C83.3NTBTattributedvalidated
ICD-112A81.5Especificvalidated
MONDO0017596Evalidated
UMLSC2026186Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card