ORPHA:289825

Late-onset primary lymphedema without systemic or visceral involvement

Type: Clinical group
Group: Group of disorders
Status: active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

Names in Orphadata languages

12 of 12 languages

Lang	Name	Synonyms
en	Late-onset primary lymphedema without systemic or visceral involvement
fr	Lymphoedème primaire tardif sans atteinte systémique ou viscérale
de	Spät-beginnendes primäres Lymphödem ohne systemische oder viszerale Beteiligung
es	Linfedema primario de inicio tardío sin afectación sistémica o visceral
it	Linfedema primitivo a esordio tardivo
nl	Primair lymfoedeem met late aanvang zonder systemische of viscerale betrokkenheid
pt	Linfedema primário de início tardio sem envolvimento sistémico ou visceral	Linfedema primário de início tardio
pl	Pierwotny obrzęk limfatyczny o późnym poczatku
cs	Primární lymfedém bez systémového nebo viscerálního postižení s pozdním nástupem
uk	Пізня первинна лімфедема без системного або вісцерального ураження
zh	不累及全身或内脏的迟发性原发性淋巴水肿
tr	Sistemik veya viseral tutulum olmayan geç-başlangıçlı primer lenfödem

Cross-references

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
UMLS	C5681007	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Classification

Preferential parent (Orphanet linearisation):

ORPHA:93890Rare developmental defect during embryogenesis

Parents in the classifications (1):

ORPHA:568041Primary lymphedema without systemic or visceral involvement
rare developmental anomalies during embryogenesis; rare genetic diseases; rare skin diseases; rare circulatory system diseases

Children (6):

Genes

0 direct

Orphanet records no gene directly on this code.

Prevalence and incidence

0 records

No prevalence record in this release.

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

Sources for this card

Orphanet page: orpha.net/en/disease/detail/289825
This record as JSON: /data/d/289825.json