Lymphoepithelial-like carcinoma
- Type
- Disease
- Group
- Disorder
- Status
- active
Lymphoepithelial-like carcinoma is a rare, malignant epithelial tumor, composed of undifferentiated epithelial cells with dense lymphoid stroma, mimicking lymphoepithelioma. It often shows association with Epstein-Barr virus infection and can develop in various organs, such as the nasopharynx, stomach, skin, breast and lungs, among others. The presenting symptoms, as well as the radiologic features, are usually nonspecific and depend on the affected site and organ.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Lymphoepithelial-like carcinoma | |
| fr | Carcinome lympho-épithélial-like | |
| de | Karzinom, lymphoepitheliom-artiges | |
| es | Carcinoma similar al linfoepitelial | |
| it | Carcinoma simil-linfoepiteliale | |
| nl | Lymfo-epitheliaalachtig carcinoom | |
| pt | Carcinoma linfoepitelial-like | |
| pl | Rak przypominający lymphoepithelioma (lymphoepithelioma-like) | |
| cs | Karcinom podobný lymfoepiteliomu | |
| uk | Лімфоепітеліоподібна карцинома | |
| zh | 淋巴上皮样癌 | |
| tr | Lenfoepitelyal-benzeri karsinom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C80.9 | NTBT | attributed | validated |
| MONDO | 0017348 | E | validated | |
| UMLS | C0334254 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:289651Epstein-Barr Virus-associated carcinoma
rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/289682
- This record as JSON: /data/d/289682.json