Infective dermatitis associated with HTLV-1
Synonyms: IDH · Infective dermatitis associated with human T-lymphotropic virus type 1 · Infective dermatitis associated with human T-lymphotropic virus type I
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Childhood
- Status
- active
Infective dermatitis associated with HTLV-1 is a rare and severe chronic disease characterized by recurrent chronic eczema (with erythematous, scaly and crusted lesions) mainly affecting seborrheic areas (e.g. scalp, forehead, eyelids, paranasal and periauricular skin, neck, axillae, and groin), a generalized fine papular rash, chronic nasal discharge with crusting of the anterior nares, and non-virulent <i>Staphylococcus aureus</i> or beta-hemolytic <i>Streptococcus</i> infections, thought to be a result of HTLV-1-induced immunosuppression. Lymphadenopathy, anemia, mild to moderate pruritus and increased incidence of other infections (e.g. crusted scabies) have also been reported in some patients. Patients may subsequently develop other HTLV-1 associated conditions such as adult T-cell leukemia/lymphoma and tropical spastic paraparesis.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Infective dermatitis associated with HTLV-1 | IDH · Infective dermatitis associated with human T-lymphotropic virus type 1 · Infective dermatitis associated with human T-lymphotropic virus type I |
| fr | Dermatite infectieuse associée au HTLV-1 | Dermatite infectieuse associée au virus T-lymphotrope humain de type 1 · Dermatite infectieuse associée au virus T-lymphotrope humain de type I · IDH |
| de | Infektiöse Dermatitis mit assoziiertem HTLV-1 | IDH · Infektiöse Dermatitis mit assoziierter humaner T-lymphotroper Virus 1-Infektion |
| es | Dermatitis infecciosa asociada al HTLV-1 | Dermatitis infecciosa asociada al virus linfotrópico de células T humanas tipo 1 · Dermatitis infecciosa asociada al virus linfotrópico de células T humanas tipo I · IDH |
| it | Dermatite infettiva associata a HTLV-1 | Dermatite infettiva associata a virus T-linfotropico umano tipo 1 · Dermatite infettiva associata a virus T-linfotropico umano tipo I · IDH |
| nl | Infectieuze dermatitis geassocieerd met HTLV-1 | IDH · Infectieuze dermatitis geassocieerd met humaan T-lymfotroop virus type 1 · Infectieuze dermatitis geassocieerd met humaan T-lymfotroop virus type I |
| pt | Dermatite infeciosa associada a HTLV-1 | Dermatite infeciosa associada a vírus linfotrópico-T humano tipo 1 · Dermatite infeciosa associada a vírus linfotrópico-T humano tipo I · IDH |
| pl | Zakaźne zapalenie skóry związane z HTLV-1 | IDH · Zakaźne zapalenie skóry związane z ludzkim wirusem T-limfotropowym typu 1 · Zakaźne zapalenie skóry związane z ludzkim wirusem T-limfotropowym typu I |
| cs | Infekční dermatitida asociovaná s HTLV-1 | IDH · Infekční dermatitida asociovaná s lidským T-lymfotropickým virem typu 1 · Infekční dermatitida asociovaná s lidským T-lymfotropickým virem typu I |
| uk | Інфекційний дерматит, асоційований з HTLV-1 | IDH · Інфекційний дерматит, асоційований з Т-лімфотропним вірусом людини типу 1 · Інфекційний дерматит, асоційований з Т-лімфотропним вірусом людини типу I |
| zh | 与HTLV-1基因相关的感染性皮炎 | 人T淋巴细胞病毒I型相关性感染性皮炎 |
| tr | HTLV-1-ilişkili enfektif dermatit | IDH · İnsan T-lenfotropik virüs tip 1 ilişkili infektif dermatit · İnsan T-lenfotropik virüs tip I ile seyreden infektif dermatit |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L30.3 | NTBT | attributed | validated |
| ICD-11 | EA88.00 | E | specific | validated |
| MONDO | 0017326 | E | validated | |
| UMLS | C4274291 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:90077Other acquired skin disease
rare skin diseases - ORPHA:163585Rare viral disease
rare infectious diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/289347
- This record as JSON: /data/d/289347.json