Well-differentiated fetal adenocarcinoma of the lung
Synonyms: WDFA
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Well-differentiated fetal adenocarcinoma of the lung is a rare, primary, low-grade, bronchopulmonary neoplasm characterized by a well-circumscribed, usually large, pulmonary mass that is histologically composed of glycogen-rich neoplastic glands and tubules that resemble fetal lungs at 10 to 16 weeks of gestation and benign adjacent stroma. It typically presents with chest pain, cough, dyspnea, hemoptysis and/or generalized, non-specific symptoms, such as night sweats, lethargy, poor appetite and weight loss.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Well-differentiated fetal adenocarcinoma of the lung | WDFA |
| fr | Adénocarcinome pulmonaire bien différencié de type foetal | = en |
| de | Fetales Adenokarzinom der Lunge, gut-differenziert | = en |
| es | Adenocarcinoma pulmonar fetal bien diferenciado | = en |
| it | Adenocarcinoma polmonare fetale differenziato | = en |
| nl | Goed gedifferentieerd foetaal adenocarcinoom van long | = en |
| pt | Adenocarcinoma bem diferenciado fetal do pulmão | |
| pl | Dobrze zróżnicowany gruczolakorak płuc płodu | = en |
| cs | Dobře diferencovaný fetální adenokarcinom plic | = en |
| uk | Добре диференційована фетальна аденокарцинома легень | = en |
| zh | 高分化胎儿肺腺癌 | = en |
| tr | Akciğerin iyi diferansiye fetal adenokarsinomu | = en |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C34.1 | BTNT | attributed | validated |
| ICD-10 | C34.2 | BTNT | attributed | validated |
| ICD-10 | C34.3 | BTNT | attributed | validated |
| ICD-10 | C34.8 | BTNT | attributed | validated |
| ICD-11 | 2C25.0 | NTBT | attributed | validated |
| MONDO | 0017292 | E | validated | |
| UMLS | C3873372 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:101945Rare bronchopulmonary and pleural cavity tumors
rare respiratory diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/284395
- This record as JSON: /data/d/284395.json