raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:280917

Idiopathic posterior uveitis

Type
Disease
Group
Disorder
Status
active

Idiopathic posterior uveitis is a rare, potentially sight-threatening, ocular disease, not attributed to any specific ocular or systemic cause, characterized by focal, multifocal or diffuse non-infectious inflammation in the posterior uvea (i.e. choroiditis, chorioretinitis, retinitis and neuroretinitis). Visual morbidity due to complications (including cystoid macular edema and choroidal neovascularization) has been reported.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enIdiopathic posterior uveitis
frUvéite postérieure idiopathique
deUveitis, posteriore, idiopathische
esUveítis posterior idiopática
itUveite posteriore idiopatica
nlIdiopathische posterieure uveïtis
ptUveíte posterior idiopática
plIdiopatyczne zapalenie tylnego odcinka błony naczyniowej
csIdiopatická zadní uveitida
ukІдіопатичний задній увеїт
zh特发性后葡萄膜炎
trİdiyopatik posterior üveit

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10H30.9NTBTattributedvalidated
ICD-119B65.0NTBTattributedvalidated
MONDO0017257Evalidated
UMLSC4751435Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card