Intermediate uveitis
Synonyms: IU
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Childhood
- Status
- active
A rare ophthalmic disorder characterized by intraocular inflammation primarily localized to the vitreous and peripheral retina. It incorporates pars planitis, posterior cyclitis, and hyalitis. Patients present with painless floaters, decreased or blurred vision, less frequently with pain, redness, and photophobia. On examination, snow banking, vitreous snowballs, peripheral retinal vascular sheathing, vitreous cells, and vitreous haze can be seen. Complications include epiretinal membrane formation, cataract formation, cystoid macular edema, or band keratopathy, among others. The condition may be idiopathic or occur in the context of infectious or systemic diseases.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Intermediate uveitis | IU |
| fr | Uvéite intermédiaire | = en |
| de | Uveitis, intermediäre | = en |
| es | Uveítis intermedia | UI |
| it | Uveite intermedia | = en |
| nl | Intermediaire uveïtis | = en |
| pt | Uveíte intermédia | = en |
| pl | Zapalenie pośredniej części błony naczyniowej oka | = en |
| cs | Intermediální uveitida | = en |
| uk | Помірно виражений увеїт | = en |
| zh | 中间葡萄膜炎 | = en |
| tr | Orta düzey üveit | = en |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | H30.2 | NTBT | attributed | validated |
| ICD-11 | 9B66 | E | specific | validated |
| MONDO | 0006806 | E | validated | |
| MeSH | D015867 | E | validated | |
| UMLS | C0042166 | E | validated | |
| MedDRA | 10022557 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:98715Uveitis
rare ophthalmic disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
18 annotations · validated 2019-07-05| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Frequent (79-30%) | ||
| HP:0040049 | Macular edema | |
| Occasional (29-5%) | ||
| HP:0012122 | Anterior uveitis | |
| HP:0000585 | Band keratopathy | |
| HP:0000518 | Cataract | |
| HP:0011505 | Cystoid macular edema | |
| HP:0100014 | Epiretinal membrane | |
| HP:0000501 | Glaucoma | |
| HP:0100653 | Optic neuritis | |
| HP:0011484 | Posterior synechiae of the anterior chamber | |
| HP:0007663 | Reduced visual acuity | |
| HP:0002633 | Vasculitis | |
| HP:0100832 | Vitreous floaters | |
| HP:0030652 | Vitreous haze | |
| HP:0030661 | Vitreous snowballs | |
| Very rare (<4-1%) | ||
| HP:0031035 | Chronic infection | |
| HP:0200056 | Macular scar | |
| HP:0003765 | Psoriasiform dermatitis | |
| HP:0001970 | Tubulointerstitial nephritis | |
Annotation source: 29370567[PMID]_28449695[PMID]_31082037[PMID]
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/279914
- This record as JSON: /data/d/279914.json