ORPHA:275844
Pulmonary hypertension with unclear multifactorial mechanism
Synonyms: PH with unclear multifactorial mechanism
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Pulmonary hypertension with unclear multifactorial mechanism | PH with unclear multifactorial mechanism |
| fr | Hypertension pulmonaire d'origine multifactorielle non élucidée | HP d'origine multifactorielle non élucidée |
| de | Pulmonale arterielle Hypertonie unklarer multifaktorieller Genese | Hypertension, arterielle pulmonale, unklarer Genese · PH unklarer multifaktorieller Genese |
| es | Hipertensión arterial pulmonar con mecanismos multifactoriales no aclarados | HAP con mecanismos multifactoriales no aclarados |
| it | Ipertensione arteriosa polmonare con meccanismo multifattoriale non noto | PH con meccanismo multifattoriale non noto |
| nl | Pulmonale arteriële hypertensie met onduidelijk multifactorieel mechanisme | PH met onduidelijk multifactorieel mechanisme |
| pt | Hipertensão arterial pulmonar com mecanismo multifatorial pouco claro | |
| pl | Tętnicze nadciśnienie płucne z niejasnym mechanizmem wieloczynnikowym | PAH z niejasnym mechanizmem wieloczynnikowym |
| cs | Plicní hypertenze s nejasným multifaktoriálním mechanismem | PH s nejasným multifaktoriálním mechanismem |
| uk | Легенева гіпертензія з незясованим багатофакторним механізмом | ЛГ з незясованим багатофакторним механізмом |
| zh | 多种不明机制所致肺动脉高压 | 多种不明机制所致PH |
| tr | Belirsiz multifaktöriyel mekanizma ile seyreden pulmoner hipertansiyon | Belirsiz çok faktörlü mekanizma ile seyreden PH |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 17158 | E | validated | |
| UMLS | C4509216 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:71198Rare pulmonary hypertension
rare respiratory diseases
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/275844
- This record as JSON: /data/d/275844.json