raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:275844

Pulmonary hypertension with unclear multifactorial mechanism

Synonyms: PH with unclear multifactorial mechanism

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPulmonary hypertension with unclear multifactorial mechanismPH with unclear multifactorial mechanism
frHypertension pulmonaire d'origine multifactorielle non élucidéeHP d'origine multifactorielle non élucidée
dePulmonale arterielle Hypertonie unklarer multifaktorieller GeneseHypertension, arterielle pulmonale, unklarer Genese · PH unklarer multifaktorieller Genese
esHipertensión arterial pulmonar con mecanismos multifactoriales no aclaradosHAP con mecanismos multifactoriales no aclarados
itIpertensione arteriosa polmonare con meccanismo multifattoriale non notoPH con meccanismo multifattoriale non noto
nlPulmonale arteriële hypertensie met onduidelijk multifactorieel mechanismePH met onduidelijk multifactorieel mechanisme
ptHipertensão arterial pulmonar com mecanismo multifatorial pouco claro
plTętnicze nadciśnienie płucne z niejasnym mechanizmem wieloczynnikowymPAH z niejasnym mechanizmem wieloczynnikowym
csPlicní hypertenze s nejasným multifaktoriálním mechanismemPH s nejasným multifaktoriálním mechanismem
ukЛегенева гіпертензія з незясованим багатофакторним механізмомЛГ з незясованим багатофакторним механізмом
zh多种不明机制所致肺动脉高压多种不明机制所致PH
trBelirsiz multifaktöriyel mekanizma ile seyreden pulmoner hipertansiyonBelirsiz çok faktörlü mekanizma ile seyreden PH
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO17158Evalidated
UMLSC4509216Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card