raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:264973

Secondary interstitial lung disease in childhood and adulthood associated with a systemic vasculitis

Synonyms: Secondary ILD in childhood and adulthood associated with a systemic vasculitis

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enSecondary interstitial lung disease in childhood and adulthood associated with a systemic vasculitisSecondary ILD in childhood and adulthood associated with a systemic vasculitis
frPneumopathie interstitielle secondaire de l'enfant et de l'adulte associée à une vascularite systémiqueILD secondaire spécifique de de l'enfant et de l'adulte associée à une vascularite systémique
deSekundäre interstitielle Lungenkrankheit des Kindes/Erwachsenen mit assoziierter systemischer VaskultitsSekundäre ILD des Kindes/Erwachsenen mit assoziierter systemischer Vaskultits
esEnfermedad pulmonar intersticial secundaria de la infancia y del adulto asociada a una vasculitis sistémicaEPI secundaria de la infancia y del adulto asociada con una vasculitis sistémica
itPneumopatia interstiziale secondaria dell'infanzia e dell'età adulta associata a vasculite sistemicaILD secondaria dell'infanzia e dell'età adulta associata a vasculite sistemica
nlSecundaire interstitiële longziekte in de kinderjaren en volwassenheid geassocieerd met systemische vasculitisSecundaire ILD in de kinderjaren en volwassenheid geassocieerd met systemische vasculitis
ptDoença pulmonar intersticial secundária da infância e do adulto associada a uma vasculite sistémica
plWtórna choroba śródmiąższowa płuc wieku dziecięcego i dorosłego związana z układowym zapaleniem naczyńWtórna ILD wieku dziecięcego i dorosłego związana z układowym zapaleniem naczyń
csSekundární instersticiální plicní nemoc v dětství a dospělosti asociovaná se systémovou vaskulitidouSekundární ILD v dětství a dospělosti asociovaná se systémovou vaskulitidou
ukВторинне інтерстиціальне захворювання легень у дитячому та дорослому віці, повязане з системним васкулітомВторинна ILD в дитячому та дорослому віці, повязана з системним васкулітом
zh系统性脉管炎相关儿童期和成年期继发性间质性肺病全身性血管炎相关儿童期和成年期继发性ILD
trSistemik vaskülit ilişkili çocukluk ve yetişkinlikte sekonder interstisyel akciğer hastalığıSistemik vaskülit ile ilişkili çocukluk ve erişkinlikte sekonder ILD
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO17038Evalidated
UMLSC5679733Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (2):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card