ORPHA:264973
Secondary interstitial lung disease in childhood and adulthood associated with a systemic vasculitis
Synonyms: Secondary ILD in childhood and adulthood associated with a systemic vasculitis
- Type
- Category
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Secondary interstitial lung disease in childhood and adulthood associated with a systemic vasculitis | Secondary ILD in childhood and adulthood associated with a systemic vasculitis |
| fr | Pneumopathie interstitielle secondaire de l'enfant et de l'adulte associée à une vascularite systémique | ILD secondaire spécifique de de l'enfant et de l'adulte associée à une vascularite systémique |
| de | Sekundäre interstitielle Lungenkrankheit des Kindes/Erwachsenen mit assoziierter systemischer Vaskultits | Sekundäre ILD des Kindes/Erwachsenen mit assoziierter systemischer Vaskultits |
| es | Enfermedad pulmonar intersticial secundaria de la infancia y del adulto asociada a una vasculitis sistémica | EPI secundaria de la infancia y del adulto asociada con una vasculitis sistémica |
| it | Pneumopatia interstiziale secondaria dell'infanzia e dell'età adulta associata a vasculite sistemica | ILD secondaria dell'infanzia e dell'età adulta associata a vasculite sistemica |
| nl | Secundaire interstitiële longziekte in de kinderjaren en volwassenheid geassocieerd met systemische vasculitis | Secundaire ILD in de kinderjaren en volwassenheid geassocieerd met systemische vasculitis |
| pt | Doença pulmonar intersticial secundária da infância e do adulto associada a uma vasculite sistémica | |
| pl | Wtórna choroba śródmiąższowa płuc wieku dziecięcego i dorosłego związana z układowym zapaleniem naczyń | Wtórna ILD wieku dziecięcego i dorosłego związana z układowym zapaleniem naczyń |
| cs | Sekundární instersticiální plicní nemoc v dětství a dospělosti asociovaná se systémovou vaskulitidou | Sekundární ILD v dětství a dospělosti asociovaná se systémovou vaskulitidou |
| uk | Вторинне інтерстиціальне захворювання легень у дитячому та дорослому віці, повязане з системним васкулітом | Вторинна ILD в дитячому та дорослому віці, повязана з системним васкулітом |
| zh | 系统性脉管炎相关儿童期和成年期继发性间质性肺病 | 全身性血管炎相关儿童期和成年期继发性ILD |
| tr | Sistemik vaskülit ilişkili çocukluk ve yetişkinlikte sekonder interstisyel akciğer hastalığı | Sistemik vaskülit ile ilişkili çocukluk ve erişkinlikte sekonder ILD |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 17038 | E | validated | |
| UMLS | C5679733 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:264949Secondary interstitial lung disease in childhood and adulthood associated with a systemic disease
rare respiratory diseases; rare transplant-related disorders
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/264973
- This record as JSON: /data/d/264973.json