Rare lichen planus
Synonyms: Rare LP
- Type
- Category
- Group
- Group of disorders
- Age of onset
- All ages
- Status
- active
Lichen planus (LP) is a common inflammatory dermatosis characterized by the development of pruritic violaceous papules or plaques on mucocutaneous surfaces. Eruptions can involve the face, neck, limbs, back, genitalia, tongue, buccal mucosa, nails, and scalp. LP comprises rare variants affecting the skin and the mucosa. Rare cutaneous LP includes linear LP (referring to blaschkoid and zosteriform distributions of lichenoid lesions), actinic LP, annular LP, atrophic LP, annular atrophic LP, lichen planopilaris (comprising Graham Little-Piccardi-Lassueur syndrome and frontal fibrosing alopecia), lichen planus pigmentosus, and lichen planus pemphigoides. Rare mucosal LP includes vulvovaginal gingival syndrome and LP sialadenitis.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Rare lichen planus | Rare LP |
| fr | Lichen plan rare | LP rare |
| de | Lichen planus, seltener | LP, seltene Form |
| es | Liquen plano raro | |
| it | Lichen planus raro | LP raro |
| nl | Zeldzame lichen planus | Zeldzame LP |
| pt | Líquen plano raro | LP raro |
| pl | Rzadka postać liszaja płaskiego | Rzadka postać LP |
| cs | Vzácný lichen planus | Vzácný LP |
| uk | Рідкісний червоний плескатий лишай | Рідкісна LP |
| zh | 罕见性扁平苔藓 | 罕见性LP |
| tr | Nadir liken planus | Nadir LP |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 16766 | E | validated | |
| UMLS | C5679638 | E | validated | |
| GARD | 12344 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:79353Epidermal disease
rare skin diseases
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/254367
- This record as JSON: /data/d/254367.json