raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:252131

Benign peripheral nerve sheath tumor

Synonyms: BPNST

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enBenign peripheral nerve sheath tumorBPNST
frTumeur bénine des gaines nerveuses périphériques= en
deNervenscheidentumor, benigner peripherer= en
esTumor benigno de vaina nerviosa periférica= en
itTumore benigno delle guaine nervose periferiche= en
nlGoedaardige tumor van perifere zenuwschede= en
ptTumor benigno da bainha dos nervos periféricos= en
plŁagodny guz osłonek nerwów obwodowych= en
csBenigní periferní nádor nervové pochvy= en
ukДоброякісна пухлина оболонки периферичного нерва= en
zh良性周围神经鞘瘤= en
trSelim periferik sinir kılıfı tümörü= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO0016752Evalidated
MONDO16752Evalidated
UMLSC5577926Evalidated
MedDRA10087084Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (4):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card