Anaplastic ganglioglioma
- Type
- Disease
- Group
- Disorder
- Status
- active
A rare mixed neuronal-glial tumor characterized by a mostly supratentorial space-occupying lesion often involving the temporal lobe, although it may occur anywhere in the central nervous system. The tumor shows anaplastic features in its glial component and is considered WHO grade III, which may, albeit inconsistently, indicate more aggressive behavior and less favorable prognosis. Clinical symptoms vary according to the location, the most common manifestation being seizures.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Anaplastic ganglioglioma | |
| fr | Gangliogliome anaplasique | |
| de | Gangliogliom, anaplastisches | |
| es | Ganglioglioma anaplásico | |
| it | Ganglioglioma anaplastico | |
| nl | Anaplastisch ganglioglioom | |
| pt | Ganglioglioma anaplásico | |
| pl | Zwojakoglejak anaplastyczny | |
| cs | Anaplastický gangliogliom | |
| uk | Анапластична гангліогліома | |
| zh | 间变性神经节神经胶质瘤 | |
| tr | Anaplastik gangliogliom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D43.0 | NTBT | attributed | not yet validated |
| ICD-11 | 2A00.21 | NTBT | index | validated |
| ICD-11 | XH2GG3 | E | specific | validated |
| MONDO | 0016734 | E | validated | |
| UMLS | C0431112 | E | validated | |
| GARD | 10639 | E | validated | |
| MedDRA | 10089832 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:251934Mixed neuronal-glial tumor
rare neurological diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/251957
- This record as JSON: /data/d/251957.json