Idiopathic recurrent pericarditis
Synonyms: Idiopathic relapsing pericarditis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
Idiopathic recurrent pericarditis is a rare autoinflammatory syndrome defined as recurrence of pericardial inflammation of unknown origin following the first episode of acute pericarditis and a symptom-free interval of 4-6 weeks or longer. Recurrent attacks of chest pain may be the sole presentation or the chest pain may be accompanied by pericardial friction rub, electrocardiographic or echocardiographic changes, pericardial effusion and increased C-reactive protein. Cardiac tamponade is a rare, life-threatening complication.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Idiopathic recurrent pericarditis | Idiopathic relapsing pericarditis |
| fr | Péricardite récurrente idiopathique | |
| de | Perikarditis, idiopathische rekurrente | |
| es | Pericarditis recurrente idiopática | |
| it | Pericardite idiopatica ricorrente | Pericardite recidivante idiopatica |
| nl | Idiopathische recidiverende pericarditis | Idiopathische terugkerende pericarditis |
| pt | Pericardite recorrente idiopática | Pericardite recidivante idiopática |
| pl | Idiopatyczne nawracające zapalenie osierdzia | = en |
| cs | Idiopatická rekurentní perikarditida | Idiopatická relabující perikarditida |
| uk | Ідіопатичний рецидивуючий перикардит | Ідіопатичний рецидивуючий перикардит |
| zh | 特发性复发性心包炎 | 特发性复发性心包炎 |
| tr | İdiyopatik tekrarlayan perikardit | İdiyopatik tekrarlayan perikardit |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I09.2 | NTBT | attributed | validated |
| ICD-11 | BB2Y | NTBT | attributed | validated |
| MONDO | 0016662 | E | validated | |
| UMLS | C4707790 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:324936Unclassified autoinflammatory syndrome
rare systemic and rheumatological diseases - ORPHA:324953Unclassified autoinflammatory syndrome of childhood
rare systemic or rheumatologic diseases of childhood
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/251307
- This record as JSON: /data/d/251307.json