Acute sensory ataxic neuropathy
Synonyms: ASAN · Acute sensory ataxic GBS · Acute sensory ataxic Guillain-Barré syndrome
- Type
- Disease
- Group
- Disorder
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- All ages
- Status
- active
A rare variant of Guillain-Barré syndrome characterized by acute onset monophasic sensory neuropathy with diminished or absent tendon reflexes, loss of proprioception, positive Romberg sign and nerve conduction features of demyelination. It presents several weeks after acute infection with paresthesias, ataxia and neuropathic pain.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Acute sensory ataxic neuropathy | ASAN · Acute sensory ataxic GBS · Acute sensory ataxic Guillain-Barré syndrome |
| fr | Neuropathie ataxique sensorielle aiguë | ASAN · SGB ataxique sensoriel aigu · Syndrome de Guillain-Barré ataxique sensoriel aigu |
| de | Neuropathie, akute ataxische sensorische | ASAN · Guillain-Barré-Syndrom, akutes ataxische sensorisches |
| es | Neuropatía atáxica sensitiva aguda | ASAN · GBS atáxico sensitivo agudo · Síndrome de Guillain-Barré atáxico sensitivo agudo |
| it | Neuropatia atassica sensoriale acuta | ASAN · GBS atassica sensoriale acuta · Sindrome atassica sensoriale acuta di Guillain-Barré |
| nl | Acute sensorische ataxische neuropathie | Acuut sensorisch ataxisch syndroom van Guillain-Barré · ASAN · Acuut sensorisch ataxisch GBS |
| pt | Neuropatia atáxica sensorial aguda | |
| pl | Ostra ataksja czuciowa | ASAN · Ostra ataksja czuciowa GBS · Ostry czuciowy ataktyczny zespół Guillaina i Barrégo |
| cs | Akutní senzorická ataxická neuropatie | ASAN · Akutní senzorický ataxický GBS · Akutní senzorický ataxický Guillainův-Barrého syndrom · Akutní senzorický ataxický Guillain-Barrého syndrom |
| uk | Гостра сенсорна атаксична нейропатія | Гострий сенсорний атаксичний GBS · Гострий сенсорний атаксичний синдром Гійєна-Барре · ASAN |
| zh | 急性感觉共济失调性神经病 | 急性感觉共济失调性吉兰-巴雷综合征 |
| tr | Akut duyusal ataksik nöropati | ASAN · Akut duyusal ataksik GBS · Akut duyusal ataksik Guillain-Barré sendromu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G61.0 | NTBT | attributed | validated |
| ICD-11 | 8C01.0 | NTBT | index | validated |
| MONDO | 0016500 | E | validated | |
| UMLS | C4707661 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:231419Functional variant of Guillain-Barré syndrome
rare neurological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/231466
- This record as JSON: /data/d/231466.json