Acute pure sensory neuropathy
Synonyms: Acute pure sensory GBS · Acute pure sensory Guillain-Barré syndrome
- Type
- Disease
- Group
- Disorder
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- All ages
- Status
- active
A rare, acquired, demyelinating neuropathy disease characterized by acute, symmetric, monophasic sensory neuropathy without motor involvement, typically manifesting with numbness in the distal lower limbs which progressively extends to all the limb, tingling sensation in the distal lower limbs, generalized areflexia, and unsteady gait, as well as clumsiness of the upper limbs, pseudoathetosis and loss of vibration sense.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Acute pure sensory neuropathy | Acute pure sensory GBS · Acute pure sensory Guillain-Barré syndrome |
| fr | Neuropathie sensorielle pure aiguë | SGB sensoriel pur aigu · Syndrome de Guillain-Barré sensoriel pur aigu |
| de | Neuronopathie, akute reine sensorische | Guillain-Barré-Syndrom, akutes reines sensorisches |
| es | Neuropatía sensitiva pura aguda | GBS sensitivo puro agudo · Síndrome de Guillain-Barré sensitivo puro agudo |
| it | Neuropatia sensoriale acuta pura | GBS sensoriale pura acuta · Sindrome di Guillain-Barré sensoriale pura acuta |
| nl | Acute zuivere sensorische neuropathie | Acuut zuiver sensorisch GBS · Acuut zuiver sensorisch syndroom van Guillain-Barré |
| pt | Neuropatia sensitiva pura aguda | GBS sensitiva pura aguda · Síndrome Guillain-Barré sensitiva pura aguda |
| pl | Ostra izolowana neuropatia czuciowa | Ostry czysty czuciowy GBS · Ostry czysty czuciowy zespół Guillaina i Barrégo |
| cs | Akutní čistá sensorická neuropatie | Akutní čistý sensorický GBS · Akutní čistý sensorický Guillainův-Barrého syndrom · Akutní čistý sensorický Guillain-Barrého syndrom |
| uk | Гостра ізольована сенсорна нейропатія | Гострий чисто сенсорний GBS · Гострий чисто сенсорний синдром Гійєна-Барре |
| zh | 急性纯感觉神经病 | 急性纯感觉性吉兰-巴雷综合征 |
| tr | Akut saf duyusal nöropati | Akut saf duyusal GBS · Akut saf duyusal Guillain-Barré sendromu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G61.0 | NTBT | attributed | validated |
| MONDO | 0016498 | E | validated | |
| UMLS | C5190881 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:231419Functional variant of Guillain-Barré syndrome
rare neurological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/231450
- This record as JSON: /data/d/231450.json