Adenoid basal carcinoma of the cervix uteri
Synonyms: Cervical adenoid basal carcinoma
- Type
- Disease
- Group
- Disorder
- Status
- active
A rare, slow-growing uterine cancer characterized, histologically, by small, well differentiated nests of basaloid cells resembling basal cell carcinoma of the skin, commonly associated with squamous cell carcinoma or squamous intraepithelial lesions. Patients are usually asymptomatic or present with dysfunctional vaginal bleeding, often with no observable lesion on the cervix. Infection with high-risk HPV-types (16 and 33) has been reported in some cases.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Adenoid basal carcinoma of the cervix uteri | Cervical adenoid basal carcinoma |
| fr | Carcinome adénoïde basal du col de l'utérus | Carcinome adénoïde basal cervical |
| de | Adenoides Basalzellkarzinom der Cervix uteri | Basalkarzinom, adenoides zervikales |
| es | Carcinoma adenoide basal de cuello de útero | Carcinoma adenoide basal cervical |
| it | Carcinoma adenoide basale della cervice uterina | Carcinoma adenoide basale cervicale |
| nl | Adenoïd basaalcelcarcinoom van baarmoederhals | Adenoïd basaalcelcarcinoom van cervix uteri · Cervicaal adenoïd basaalcelcarcinoom |
| pt | Carcinoma adenóide basal do colo do útero | |
| pl | Rak gruczołowato-podstawnokomórkowy szyjki macicy | Rak gruczołowato-podstawnokomórkowy szyjki |
| cs | Adenoidně bazální karcinom hrdla děložního | Cervikální adenoidně bazální karcinom |
| uk | Аденоїдна базальна карцинома шийки матки | Базальна карцинома аденоїдів шийки матки |
| zh | 子宫颈腺样基底癌 | 宫颈腺样基底癌 |
| tr | Serviks uterinin adenoid bazal karsinomu | Servikal adenoid bazal karsinom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C53.0 | BTNT | attributed | validated |
| ICD-10 | C53.1 | BTNT | attributed | validated |
| ICD-10 | C53.8 | BTNT | attributed | validated |
| ICD-11 | 2C77.1 | NTBT | index | validated |
| MONDO | 0016287 | E | validated | |
| MONDO | 16287 | E | validated | |
| MONDO | 6132 | E | validated | |
| UMLS | C1516403 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213761Rare cancer of cervix uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213828
- This record as JSON: /data/d/213828.json