Adenosarcoma of the cervix uteri
Synonyms: Cervical adenosarcoma
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adolescent, Adult, Elderly
- Status
- active
A rare subtype of malignant mixed epithelial and mesenchymal tumor composed of benign or mildly atypical glandular elements and a surrounding low-grade malignant stroma, often containing heterologous elements, such as areas of sex-cord-like or smooth muscle differentiation. It usually presents with vaginal bleeding or discharge, lower abdominal pain and/or a cervical mass or polyp. The tumor may arise from pre-existing endometriosis and patients may have a history of recurrent cervical polyps.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Adenosarcoma of the cervix uteri | Cervical adenosarcoma |
| fr | Adénosarcome du col de l'utérus | Adénosarcome cervical |
| de | Adenosarkom der Cervix uteri | Adenosarkom, zervikales |
| es | Adenosarcoma de cuello de útero | Adenosarcoma cervical |
| it | Adenosarcoma della cervice uterina | Adenosarcoma cervicale |
| nl | Adenosarcoom van cervix uteri | Adenosarcoom van baarmoederhals · Cervicaal adenosarcoom |
| pt | Adenossarcoma do colo do útero | |
| pl | Gruczolakomięsak szyjki macicy | Gruczolakomięsak szyjki |
| cs | Adenosarkom hrdla děložního | Cervikální adenosarkom |
| uk | Аденосаркома шийки матки | Аденосаркома шийки матки |
| zh | 子宫颈腺肉瘤 | 宫颈腺肉瘤 |
| tr | Serviks uteri adenosarkomu | Servikal adenosarkom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C53.0 | BTNT | attributed | validated |
| ICD-10 | C53.1 | BTNT | attributed | validated |
| ICD-10 | C53.8 | BTNT | attributed | validated |
| ICD-11 | 2C77.Y | NTBT | index | validated |
| MONDO | 0002876 | E | validated | |
| UMLS | C1516426 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213782Malignant mixed epithelial and mesenchymal tumor of cervix uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | — | Worldwide | Class only | Validated | ORPHANET_19685064[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213792
- This record as JSON: /data/d/213792.json