Carcinosarcoma of the cervix uteri
Synonyms: Cervical carcinosarcoma · Cervical malignant Müllerian mixed tumor · Malignant Müllerian mixed tumor of the cervix uteri
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adult, Elderly
- Status
- active
Carcinosarcoma of the cervix uteri is a rare, malignant, mixed epithelial and mesenchymal tumor, located in the cervix uteri, composed of an admixture of carcinomatous and sarcomatous elements. It usually presents with abnormal vaginal bleeding and a round, well-defined, grey to yellowish-white, pedunculated polypoid mass protruding through the cervical canal. Association with HPV infection (especially serotype 16) has been frequently reported.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Carcinosarcoma of the cervix uteri | Cervical carcinosarcoma · Cervical malignant Müllerian mixed tumor · Malignant Müllerian mixed tumor of the cervix uteri |
| fr | Carcinosarcome du col de l'utérus | Carcinosarcome cervicale · Carcinosarcome du col utérin · Tumeur müllérienne mixte maligne cervicale · Tumeur müllérienne mixte maligne du col de l'utérus |
| de | Karzinosarkom der Cervix uteri | Karzinosarkom, zervikales · MMMT der Cervix uteri · Maligner Müller-Mischtumor der Cervix uteri · Müller-Mischtumor, zervikaler |
| es | Carcinosarcoma del cuello uterino | Carcinosarcoma cervical · Tumor mülleriano mixto maligno cervical · Tumor mülleriano mixto maligno del cuello uterino |
| it | Carcinosarcoma della cervice uterina | |
| nl | Carcinosarcoom van cervix uteri | Carcinosarcoom van baarmoederhals · Cervicaal carcinosarcoom · Cervicale maligne mengtumor van Müller · Maligne mengtumor van Müller van baarmoederhals · Maligne mengtumor van Müller van cervix uteri |
| pt | Tumor maligno misto mulleriano do colo do útero | |
| pl | Mięsakorak szyjki macicy | Rak mieszany Müllera szyjki macicy · Złośliwy rak mieszany Müllera szyjki macicy |
| cs | Maligní smíšený mülleriánský nádor hrdla děložního | Cervikální maligní smíšený mulleriánský nádor |
| uk | Карциносаркома шийки матки | Карциносаркома шийки матки · Злоякісна мюллерівська змішана пухлина шийки матки · Злоякісна мюллерівська змішана пухлина шийки матки |
| zh | 子宫颈癌肉瘤 | 子宫颈恶性苗勒管混合性肿瘤 |
| tr | Serviks uterinin karsinosarkomu | Servikal karsinosarkom · Servikal habis Müllerian karma tümör · Serviks uteri habis Müllerian karma tümörü |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C53 | BTNT | attributed | validated |
| ICD-11 | 2C77.Y | NTBT | index | validated |
| MONDO | 0002877 | E | validated | |
| UMLS | C1332917 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213782Malignant mixed epithelial and mesenchymal tumor of cervix uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | — | Worldwide | Class only | Validated | ORPHANET_26023676[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213787
- This record as JSON: /data/d/213787.json