High-grade neuroendocrine carcinoma of the cervix uteri
Synonyms: High-grade neuroendocrine carcinoma of the uterine cervix · Poorly differentiated neuroendocrine carcinoma of the cervix uteri · Poorly differentiated neuroendocrine cervical carcinoma
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adult, Elderly
- Status
- active
High-grade neuroendocrine carcinoma of the cervix uteri is a rare, aggressive, primary cervical neoplasm, originating from neuroendocrine cells present in the lining epithelium of the cervix, characterized, macroscopically, by usually large lesions, sometimes with a barrel-shaped appearance. Patients often present with abnormal vaginal bleeding or discharge, pelvic/abdominal pain, post-coital spotting and/or dysuria, while symptoms related to carcinoid syndrome are not frequent.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | High-grade neuroendocrine carcinoma of the cervix uteri | High-grade neuroendocrine carcinoma of the uterine cervix · Poorly differentiated neuroendocrine carcinoma of the cervix uteri · Poorly differentiated neuroendocrine cervical carcinoma |
| fr | Carcinome neuroendocrine de haut grade du col de l'utérus | Carcinome neuroendocrine cervical peu différencié · Carcinome neuroendocrine peu différencié du col de l'utérus |
| de | High-grade-NET der Cervix uteri | Karzinom der Cervix uteri, neuroendokrines, wenig differenziertes · Zervixkarzinom, neuroendokrines, high-grade · Zervixkarzinom, neuroendokrines, wenig differenziertes |
| es | Carcinoma neuroendocrino de cuello uterino de alto grado | Carcinoma cervical neuroendocrino pobremente diferenciado · Carcinoma neuroendocrino de alto grado del cuello uterino · Carcinoma neuroendocrino pobremente diferenciado del cuello uterino |
| it | Carcinoma endocrino scarsamente differenziato della cervice uterina | Carcinoma cervicale endocrino scarsamente differenziato |
| nl | Hooggradig neuro-endocrien carcinoom van cervix uteri | Hooggradig neuro-endocrien carcinoom van baarmoederhals · Slecht gedifferentieerd neuro-endocrien carcinoom van baarmoederhals · Slecht gedifferentieerd neuro-endocrien carcinoom van cervix uteri · Slecht gedifferentieerd neuro-endocrien cervicaal carcinoom |
| pt | Carcinoma endócrino mal diferenciado do colo do útero | |
| pl | Neuroendokrynny rakowiak szyjki macicy o wysokim stopniu złośliwości | Słabo zróżnicowany neuroendokrynny rakowiak szyjki macicy |
| cs | Špatně diferencovaný endokrinní karcinom hrdla děložního | Špatně diferencovaný endokrinní cervikální karcinom |
| uk | Нейроендокринна карцинома шийки матки високого ступеня злоякісності | Нейроендокринна карцинома шийки матки високого ступеня злоякісності · Погано диференційована нейроендокринна карцинома шийки матки · Погано диференційована нейроендокринна карцинома шийки матки |
| zh | 子宫颈高度神经内分泌癌 | 子宫颈低分化神经内分泌癌 |
| tr | Serviks uterinin yüksek seviyede nöroendokrin karsinomu | Kötü diferansiye nöroendokrin servikal karsinom · Rahim ağzının yüksek dereceli nöroendokrin karsinomu · Serviks uteri'nin kötü diferansiye nöroendokrin karsinomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C53.0 | BTNT | attributed | validated |
| ICD-10 | C53.1 | BTNT | attributed | validated |
| ICD-10 | C53.8 | BTNT | attributed | validated |
| ICD-11 | 2C77.3 | NTBT | attributed | validated |
| MONDO | 0016276 | E | validated | |
| UMLS | C4751235 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:100101Neuroendocrine tumor with other location
rare endocrine diseases; rare neoplastic diseases - ORPHA:213761Rare cancer of cervix uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213777
- This record as JSON: /data/d/213777.json