Low-grade neuroendocrine tumor of the corpus uteri
Synonyms: Low-grade neuroendocrine tumor of the uterine corpus · Well-differentiated neuroendocrine neoplasm of the endometrium · Well-differentiated neuroendocrine tumor of the corpus uteri · Well-differentiated neuroendocrine tumor of the endometrium
- Type
- Disease
- Group
- Disorder
- Status
- active
Low-grade neuroendocrine tumor of the corpus uteri is an extremely rare uterine cancer typically characterized by a well demarcated, solid, frequently pedunculated tumor originating from neuroendocrine cells scattered within the endometrium, often associated with ectopic hormone production. Patients usually present with vaginal bleeding or discharge and a pelvic mass with a polypoid tumor sometimes protruding through the cervical canal. Symptoms related to ectopic hormone production (flushing, sweating, diarrhea, bronchospasm) may also develop.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Low-grade neuroendocrine tumor of the corpus uteri | Low-grade neuroendocrine tumor of the uterine corpus · Well-differentiated neuroendocrine neoplasm of the endometrium · Well-differentiated neuroendocrine tumor of the corpus uteri · Well-differentiated neuroendocrine tumor of the endometrium |
| fr | Tumeur neuroendocrine de faible grade du corps de l'utérus | Néoplasie endocrine bien différenciée de l'endomètre · Néoplasme neuroendocrine de bas grade du corps de l'utérus · Tumeur endocrine bien différenciée du corps de l'utérus · Tumeur neuroendocrine bien différenciée de l'endomètre |
| de | Low-grade-NET des Corpus uteri | Gut differenzierte neuroendokrine Neoplasie des Corpus uteri · Gut differenzierte neuroendokrine Neoplasie des Endometriums · Gut differenzierter neuroendokriner Tumor des Corpus uteri · Low-grade neuroendokriner Tumor des Corpus uteri |
| es | Carcinoma neuroendocrino de bajo grado del cuerpo uterino | Neoplasia neuroendocrina bien diferenciada del endometrio · Tumor neuroendocrino bien diferenciado del cuerpo uterino · Tumor neuroendocrino bien diferenciado del endometrio |
| it | Tumore neuroendocrino del corpo dell'utero a basso grado di malignità | Neoplasia endocrina ben differenziata dell'endometrio · Tumore endocrino ben differenziato del corpo uterino · Tumore endocrino ben differenziato dell'endometrio |
| nl | Laaggradige neuro-endocriene tumor van corpus uteri | Goed gedifferentieerd neuro-endocrien neoplasma van endometrium · Goed gedifferentieerde neuro-endocriene tumor van baarmoederlichaam · Goed gedifferentieerde neuro-endocriene tumor van corpus uteri · Goed gedifferentieerde neuro-endocriene tumor van endometrium · Laaggradige neuro-endocriene tumor van baarmoederlichaam |
| pt | Neoplasia endócrino bem diferenciada do corpo uterino | |
| pl | Neuroendokrynny rakowiak trzonu macicy o niskim stopniu złośliwości | Dobrze zróżnicowany neuroendokrynny rak endometrium · Dobrze zróżnicowany neuroendokrynny rak trzonu macicy · Dobrze zróżnicowany neuroendokrynny nowotwór endometrium |
| cs | Dobře diferencovaná endokrinní neoplázie těla děložního | Dobře diferencovaná endokrinní neoplázie endometria · Dobře diferencovaný endokrinní nádor těla děložního · Dobře diferencovaný endokrinní nádor endometria |
| uk | Нейроендокринна пухлина тіла матки низького ступеня злоякісності | Нейроендокринна пухлина тіла матки низького ступеня злоякісності · Добре диференційована нейроендокринна пухлина ендометрію · Добре диференційована нейроендокринна пухлина тіла матки · Добре диференційована нейроендокринна пухлина ендометрію |
| zh | 子宫体低度神经内分泌肿瘤 | 子宫体高分化神经内分泌肿瘤 |
| tr | Korpus uteri'nin düşük seviyede nöroendokrin tümörü | Uterus korpusunun düşük dereceli nöroendokrin tümörü · Endometriumun iyi diferansiye nöroendokrin tümörü · Korpus uteri'nin iyi diferansiye nöroendokrin tümörü · Endometriumun iyi diferansiye nöroendokrin neoplazmı |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C54.0 | BTNT | attributed | validated |
| ICD-10 | C54.1 | BTNT | attributed | validated |
| ICD-10 | C54.2 | BTNT | attributed | validated |
| ICD-10 | C54.3 | BTNT | attributed | validated |
| ICD-10 | C54.8 | BTNT | attributed | validated |
| ICD-11 | 2C76.Y | NTBT | attributed | validated |
| MONDO | 0016270 | E | validated | |
| UMLS | C5190779 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213569Rare cancer of corpus uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213736
- This record as JSON: /data/d/213736.json