Leiomyosarcoma of the corpus uteri
- Type
- Disease
- Group
- Disorder
- Status
- active
Leiomyosarcoma of the corpus uteri is a rare, malignant, mesenchymal tumor of smooth muscle origin characterized, histologically, by spindle and/or pleomorphic cells, often forming disorganized fascicles, with tumor cell necrosis and, macroscopically, by a large, soft, usually intramural mass with irregular borders and necrotic and hemorrhagic areas, located in the uterus. Presenting signs and symptoms typically include dysfunctional vaginal bleeding, vaginal discharge, palpable pelvic mass and/or pelvic pain/pressure. Changes in bowel habits, frequent or painful urination and hematuria may also be associated.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Leiomyosarcoma of the corpus uteri | |
| fr | Léiomyosarcome du corps de l'utérus | |
| de | Leiomyosarkom des Corpus uteri | |
| es | Leiomiosarcoma de cuerpo de útero | |
| it | Leiomiosarcoma del corpo dell'utero | |
| nl | Leiomyosarcoom van corpus uteri | Leiomyosarcoom van baarmoederlichaam |
| pt | Leiomiossarcoma do corpo uterino | |
| pl | Mięsak gładkokomórkowy trzonu macicy | |
| cs | Leiomyosarkom těla děložního | |
| uk | Лейоміосаркома тіла матки | |
| zh | 子宫体平滑肌肉瘤 | |
| tr | Korpus uteri leiomyosarkomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C54.2 | BTNT | attributed | validated |
| ICD-11 | 2B58.1 | E | specific | validated |
| MONDO | 0016262 | E | validated | |
| UMLS | C0280631 | E | validated | |
| MedDRA | 10046799 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213620Sarcoma of the corpus uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213625
- This record as JSON: /data/d/213625.json