Carcinosarcoma of the corpus uteri
Synonyms: Malignant mixed Müllerian tumor of the corpus uteri · Mixed Müllerian cancer of corpus uteri · Uterine carcinosarcoma
- Type
- Disease
- Group
- Disorder
- Status
- active
Carcinosarcoma of the corpus uteri is a rare, malignant, mixed epithelial and mesenchymal tumor of the uterine body composed of high-grade carcinomatous and sarcomatous elements. It may present with vaginal bleeding, abnormal vaginal discharge, abdominal pain and/or pelvic mass, with a polypoid tumor sometimes protruding through the cervical canal. Association with Tamoxifen therapy, long-term unopposed estrogen use and previous pelvic radiotherapy has been reported.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Carcinosarcoma of the corpus uteri | Malignant mixed Müllerian tumor of the corpus uteri · Mixed Müllerian cancer of corpus uteri · Uterine carcinosarcoma |
| fr | Carcinosarcome du corps de l'utérus | Carcinosarcome utérin · Tumeur müllérienne mixte maligne du corps de l'utérus |
| de | Karzinosarkom des Corpus uteri | Müller-Mischtumor des Corpus uteri · Karzinosarkom, uterines · MMMT des Uterus |
| es | Carcinosarcoma del cuerpo uterino | Carcinosarcoma uterino · Cáncer mülleriano mixto del cuerpo uterino · Tumor mülleriano mixto maligno del cuerpo uterino |
| it | Carcinoma del corpo dell'utero | |
| nl | Carcinosarcoom van corpus uteri | Carcinosarcoom van baarmoederlichaam · Gemengde Mülleriaanse kanker van baarmoederlichaam · Gemengde Mülleriaanse kanker van corpus uteri · Maligne mengtumor van Müller van baarmoederlichaam · Maligne mengtumor van Müller van corpus uteri · Uterien carcinosarcoom |
| pt | Tumor misto mulleriano do corpo uterino | |
| pl | Mięsakorak trzonu macicy | Mięsakorak macicy · Rak mieszany Müllera trzonu macicy · Złośliwy rak mieszany Müllera trzonu macicy |
| cs | Zhoubný smíšený mülleriánský nádor těla děložního | Smíšená mülleriánská rakovina těla děložního |
| uk | Карциносаркома тіла матки | Злоякісна змішана мюллерова пухлина тіла матки · Змішаний мюллерівський рак тіла матки · Карциносаркома матки |
| zh | 子宫体癌肉瘤 | 子宫体恶性混合型苗勒管肿瘤 |
| tr | Korpus uteri karsinosarkomu | Uterin karsinosarkom · Korpus uteri'nin karma Müllerian kanseri · Korpus uteri'nin habis karma Müllerian tümörü |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C54.9 | BTNT | attributed | validated |
| ICD-11 | 2C76.43 | E | specific | validated |
| MONDO | 0016259 | E | validated | |
| UMLS | C1704376 | E | validated | |
| GARD | 12335 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213589Malignant mixed epithelial and mesenchymal tumor of corpus uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213610
- This record as JSON: /data/d/213610.json