raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:2039

OBSOLETE: Congenital systemic arteriovenous fistula

inactive · referred to ORPHA:68419Rare vascular anomaly

Type
Morphological anomaly
Group
Disorder
Status
inactive
Flag
Obsolete entity

This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Rare vascular anomaly

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enOBSOLETE: Congenital systemic arteriovenous fistula
frOBSOLETE : Fistule artérioveineuse systémique congénitale
deOBSOLET: Kongenitale systemische arteriovenöse Fistel
esOBSOLETO: Fístula arteriovenosa sistémica congénita
itOBSOLETO: Fistola arterovenosa sistemica congenita
nlOBSOLEET: Congenitale systemische arterioveneuze fistel
ptOBSOLETO: Fístula arterio-venosa sistémica
plNIEAKTUALNE: Wrodzona systemowa przetoka tętniczo-żylna
csNEAKTUÁLNÍ: Vrozená systémová arteriovenózní píštěl
ukВроджена системна артеріовенозна фістула
zh先天性体循环动静脉瘘
trDoğumsal sistemik arteriyovenöz fistül

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card