raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:189439

OBSOLETE: Primary pigmented nodular adrenocortical disease

inactive · referred to ORPHA:647772Isolated primary pigmented nodular adrenocortical disease

Synonyms: OBSOLETE: PPNAD · OBSOLETE: Primary pigmented nodular adrenal dysplasia

Type
Disease
Group
Disorder
Status
inactive
Flag
Obsolete entity

This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Isolated primary pigmented nodular adrenocortical disease

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enOBSOLETE: Primary pigmented nodular adrenocortical diseaseOBSOLETE: PPNAD · OBSOLETE: Primary pigmented nodular adrenal dysplasia
frOBSOLETE : Dysplasie micronodulaire pigmentée des surrénalesOBSOLETE : Maladie adrénocorticale nodulaire pigmentée primaire · OBSOLETE : PPNAD
deOBSOLET: Primäre pigmentierte noduläre adrenokortikale KrankheitOBSOLET: PPNAD · OBSOLET: Primäre pigmentierte noduläre adrenokortikale Dysplasie
esOBSOLETO: Enfermedad corticosuprarrenal nodular pigmentada primariaOBSOLETO: Displasia suprarrenal nodular pigmentada primaria · OBSOLETO: PPNAD
itOBSOLETO: Malattia adrenocorticale nodulare pigmentata primitivaOBSOLETO: Displasia surrenalica nodulare pigmentata primitiva · OBSOLETO: PPNAD
nlOBSOLEET: Primaire gepigmenteerde nodulaire adrenocorticale ziekteOBSOLEET: PPNAD · OBSOLEET: Primaire gepigmenteerde nodulaire adrenale dysplasie
ptOBSOLETO: Doença supra-renal nodular pigmentada primáriaOBSOLETO: Displasia supra-renal nodular pigmentada · OBSOLETO: PPNAD
plNIEAKTUALNE: Pierwotna barwnikowa guzkowa choroba kory nadnerczyNIEAKTUALNE: PPNAD
csNEAKTUÁLNÍ: Primární pigmentovaná nodulární adrenokortikální nemocNEAKTUÁLNÍ: PPNAD
ukЗАСТАРІЛО: Первинна пігментна вузликова адренокортикальна хворобаЗАСТАРІЛО: PPNAD · ЗАСТАРІЛО: Первинна пігментно-вузлова дисплазія надниркових залоз
zh原发性色素性结节性肾上腺皮质疾病原发性色素性结节性肾上腺发育不良
trPrimer pigmentli nodüler adrenokortikal hastalıkPPNAD · Primer pigmentli nodüler adrenal displazi

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

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Classification

Not placed in any Orphanet classification in this release.

No children.

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Genes

0 direct

Orphanet records no gene directly on this code.

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Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

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Sources for this card