raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:182095

Interstitial lung disease

Synonyms: ILD

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enInterstitial lung diseaseILD
frPneumopathie interstitielle= en
deInterstitielle Lungenkrankheit= en
esEnfermedad pulmonar intersticialEPI · ILD
itPneumopatia interstiziale= en
nlInterstitiële longziekte= en
ptPulmonar intersticial, doença
plŚródmiąższowa choroba płuc= en
csIntersticiální plicní nemoci= en
ukІнтерстиціальне захворювання легень= en
zh间质性肺病= en
trİnterstisyel akciğer hastalığı= en
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO0015925Evalidated
MONDO15925Evalidated
MeSHD017563Evalidated
UMLSC0206062Evalidated
MedDRA10022611Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

Children (3):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

5 records
TypeClassValueAreaQualificationValidationSource
Annual incidence1-9 / 100 0004.1 / 100 000DenmarkValue and classValidated24636811[PMID]
Annual incidence1-9 / 100 0005.4 / 100 000EuropeValue and classNot yet validated24636811[PMID]
Annual incidence1-9 / 100 0007.6 / 100 000SpainValue and classValidated15127977[PMID]
Annual incidence1-9 / 100 0004.63 / 100 000GreeceValue and classValidated19345567[PMID]
Point prevalence1-5 / 10 00017.3 / 100 000GreeceValue and classValidated19345567[PMID]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card