Folliculotropic mycosis fungoides
Synonyms: Mycosis fungoides-associated follicular mucinosis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A variant of mycosis fungoides (MF) characterized by the presence of folliculotropic infiltrates, often with sparing of the epidermis and preferential involvement of the head and neck region. Most cases show mucinous degeneration of the hair follicles (follicular mucinosis) and are traditionally designated as MF-associated follicular mucinosis.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Folliculotropic mycosis fungoides | Mycosis fungoides-associated follicular mucinosis |
| fr | Mycosis fongoïde folliculotrope | Mycosis fongoïde avec mucinose folliculaire |
| de | Mycosis fungoides, follikulotrope | Muzinose, follikuläre, Mycosis fungoides-assoziierte |
| es | Micosis fungoide foliculotropa | Mucinosis folicular asociada a micosis fungoide |
| it | Micosi fungoide follicolotropica | |
| nl | Folliculotrope mycosis fungoides | Mycosis fungoides-geassocieerde folliculaire mucinose |
| pt | Micose fungóide foliculotrópica | |
| pl | Ziarniniak grzybiasty folikulotropowy | Ziarniniak grzybiasty z towarzyszącą mucynozą pęcherzykową |
| cs | Mycosis fungoides - folikulotropní varianta | Mycosis fungoides asociovaná s folikulární mucinózou |
| uk | Фолікулотропний мікоз фунгоїдів | Фолікулярний муциноз, асоційований з мікозом фунгоїдів |
| zh | 亲毛囊性蕈样肉芽肿 | 蕈样肉芽肿相关毛囊皮脂腺粘蛋白累积病 |
| tr | Folikülotropik mikozis fungoides | Mikoz fungoides-ilişkili foliküler müsinoz |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C84.0 | NTBT | attributed | validated |
| ICD-11 | 2B01 | NTBT | index | validated |
| MONDO | 0015808 | E | validated | |
| UMLS | C1627767 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:178566Mycosis fungoides and variants
rare skin diseases; rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/178512
- This record as JSON: /data/d/178512.json