ORPHA:168811
Malignant peritoneal mesothelioma
Synonyms: Diffuse malignant peritoneal mesothelioma · Primary malignant peritoneal mesothelioma
- Type
- Disease
- Group
- Disorder
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- Adult
- Status
- active
Malignant peritoneal mesothelioma is a primary peritoneal malignancy occurring in the lining cells (mesothelium) of the peritoneal cavity.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Malignant peritoneal mesothelioma | Diffuse malignant peritoneal mesothelioma · Primary malignant peritoneal mesothelioma |
| fr | Mésothéliome péritonéal malin | Mésothéliome malin primitif · Mésothéliome péritonéal malin diffus |
| de | Peritonealmesotheliom, malignes | Mesotheliom, malignes primäres |
| es | Mesotelioma peritoneal maligno | Mesotelioma peritoneal maligno difuso · Mesotelioma peritoneal maligno primario |
| it | Mesotelioma peritoneale maligno | Mesotelioma peritoneale maligno diffuso · Mesotelioma peritoneale maligno primitivo |
| nl | Maligne peritoneaal mesothelioom | Diffuus maligne peritoneaal mesothelioom · Kwaadaardig peritoneaal mesothelioom · Primair maligne peritoneaal mesothelioom |
| pt | Mesotelioma peritoneal maligno | |
| pl | Złośliwy międzybłoniak otrzewnej | Pierwotny złośliwy międzybłoniak otrzewnej · Rozlany złośliwy międzybłoniak otrzewnej |
| cs | Peritoneální maligní mezoteliom | Difuzní peritoneální maligní mezoteliom · Primární peritoneální maligní mezoteliom |
| uk | Злоякісна перитоніальна мезотеліома | Дифузна злоякісна мезотеліома очеревини · Первинна злоякісна мезотеліома очеревини |
| zh | 恶性腹膜间皮瘤 | 原发性恶性腹膜间皮瘤 |
| tr | Habis peritoneal mezotelyoma | Yaygın habis peritoneal mezotelyoma · Primer habis peritoneal mezotelyoma |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C45.1 | E | specific | validated |
| ICD-11 | 2C51.2 | E | specific | validated |
| MONDO | 0005512 | E | validated | |
| UMLS | C0346109 | E | validated | |
| MedDRA | 10056558 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:168807Primary malignant peritoneal tumor
rare abdominal surgical diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
3 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 1 000 000 | 0.2 / 100 000 | France | Value and class | Validated | [EXPERT] |
| Point prevalence | 1-9 / 100 000 | — | Europe | Class only | Validated | European Medicines Agency 2016[OTHER] |
| Annual incidence | 1-9 / 1 000 000 | 0.5 / 100 000 | Italy | Value and class | Validated | [EXPERT] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
6
HPO phenotypes
10 annotations · validated 2016-06-01| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0003270 | Abdominal distention | |
| HP:0002027 | Abdominal pain | |
| HP:0001541 | Ascites | |
| HP:0002664 | Neoplasm | |
| HP:0002586 | Peritonitis | |
| Frequent (79-30%) | ||
| HP:0001824 | Weight loss | |
| Occasional (29-5%) | ||
| HP:0001928 | Abnormality of coagulation | |
| HP:0002094 | Dyspnea | |
| HP:0002595 | Ileus | |
| HP:0010741 | Pedal edema | |
Run the differential on the 5 obligate / very frequent terms
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/168811
- This record as JSON: /data/d/168811.json