ORPHA:157987
Non-Langerhans cell histiocytosis
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Non-Langerhans cell histiocytosis | |
| fr | Histiocytose non langerhansienne | |
| de | Non-Langerhans-Zell-Histiozytose | |
| es | Histiocitosis de células no Langerhans | |
| it | Istiocitosi delle cellule non Langerhans | |
| nl | Niet-Langerhanscelhistiocytose | |
| pt | Histiocitose de células não-Langerhans | |
| pl | Histiocytoza nie wywodząca się z komórek Langerhansa | |
| cs | Histiocytóza z non-Langerhansových buněk | |
| uk | Гістіоцитоз нелангергансових клітин | |
| zh | 非朗格汉斯细胞组织细胞增多症 | |
| tr | Langerhans hücreli olmayan histiyositoz |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 0015531 | E | validated | |
| MONDO | 15531 | E | validated | |
| MeSH | D015616 | E | validated | |
| UMLS | C0019624 | E | validated | |
| GARD | 8231 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:182222Rare systemic disease
rare systemic and rheumatological diseases - ORPHA:290836Systemic disease with skin involvement
rare skin diseases
Children (12):
- ORPHA:157997Benign cephalic histiocytosis
- ORPHA:35687Erdheim-Chester disease
- ORPHA:157991Generalized eruptive histiocytosis
- ORPHA:158025Hereditary progressive mucinous histiocytosis
- ORPHA:158019Indeterminate cell histiocytosis
- ORPHA:158000Juvenile xanthogranuloma
- ORPHA:139436Multicentric reticulohistiocytosis
- ORPHA:158011Necrobiotic xanthogranuloma
- ORPHA:158008Papular xanthoma
- ORPHA:158022Progressive nodular histiocytosis
- ORPHA:158014Rosaï-Dorfman disease
- ORPHA:158003Xanthoma disseminatum
Codes that Orphanet moved or referred to this one:
- ORPHA:158029OBSOLETE: Sea-blue histiocytosis referred to · inactive
- ORPHA:240266OBSOLETE: Systemic non-Langerhans cell histiocytosis referred to · inactive
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/157987
- This record as JSON: /data/d/157987.json