Paroxysmal hemicrania
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adolescent, Adult, Childhood, Elderly
- Status
- active
A rare primary headache disorder characterized by multiple attacks of unilateral pain that occur in association with ipsilateral cranial autonomic symptoms. The hallmarks of this syndrome are the relative shortness of the attacks and the complete response to indomethacin therapy.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Paroxysmal hemicrania | |
| fr | Hémicrânie paroxystique | |
| de | Hemikranie, paroxysmale | |
| es | Hemicrania paroxística | |
| it | Emicrania parossistica | |
| nl | Paroxysmale hemicranie | |
| pt | Hemicranea paroxística | |
| pl | Hemikrania napadowa | |
| cs | Paroxysmální hemikranie | |
| uk | Пароксизмальна гемікранія | |
| zh | 阵发性偏头痛 | |
| tr | Paroksismal hemikrani |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G44.0 | NTBT | attributed | validated |
| ICD-11 | 8A82 | NTBT | index | validated |
| MONDO | 0015529 | E | validated | |
| MeSH | D051302 | E | validated | |
| UMLS | C1399352 | E | validated | |
| GARD | 10794 | E | validated | |
| MedDRA | 10019461 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:157843Trigeminal autonomic cephalalgia
rare neurological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Europe | Class only | Validated | [EXPERT]_29720814[PMID] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
21 annotations · validated 2018-02-26| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0002076 | Migraine | |
| HP:0002331 | Recurrent paroxysmal headache | |
| Frequent (79-30%) | ||
| HP:0030953 | Conjunctival hyperemia | |
| HP:0009926 | Epiphora | |
| HP:0031284 | Flushing | |
| HP:0002183 | Phonophobia | |
| HP:0000613 | Photophobia | |
| HP:0000508 | Ptosis | |
| HP:0012384 | Rhinitis | |
| HP:0031417 | Rhinorrhea | |
| Occasional (29-5%) | ||
| HP:0000819 | Diabetes mellitus | |
| HP:0000822 | Hypertension | |
| HP:0000616 | Miosis | |
| HP:0002017 | Nausea and vomiting | |
| HP:0030833 | Neck pain | |
| HP:0011161 | Olfactory auras | |
| HP:0100540 | Palpebral edema | |
| HP:0012452 | Restless legs | |
| HP:0025258 | Stiff neck | |
| Excluded (0%) | ||
| HP:0012199 | Cluster headache | |
| HP:0100661 | Trigeminal neuralgia | |
Run the differential on the 2 obligate / very frequent terms
Annotation source: 24523000[PMID]_23566235[PMID]
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/157835
- This record as JSON: /data/d/157835.json