ORPHA:100067
Waterhouse-Friderichsen syndrome
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Status
- active
This disease is described under Acute adrenal insufficiency
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Waterhouse-Friderichsen syndrome | |
| fr | Syndrome de Waterhouse-Friderichsen | |
| de | Waterhouse-Friderichsen-Syndrom | |
| es | Síndrome de Waterhouse-Friderichsen | |
| it | Sindrome di Waterhouse-Friderichsen | |
| nl | Waterhouse-Friderichsensyndroom | |
| pt | Síndrome de Waterhouse-Friedrickson | |
| pl | Zespół Waterhouse-Friderichsena | |
| cs | Waterhouseův-Friderichsenův syndrom | Waterhouse-Friderichsenův syndrom |
| uk | Синдром Уотерхауса-Фрідріхсена | |
| zh | 华-弗综合征 | |
| tr | Waterhouse-Friderichsen sendromu |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | A39.1+ | E | specific | validated |
| ICD-10 | E35.1* | NTBT | inclusion | validated |
| ICD-11 | 1C1C.1 | E | specific | validated |
| MONDO | 0006015 | E | validated | |
| MeSH | D014884 | E | validated | |
| UMLS | C1403891 | E | validated | |
| GARD | 9449 | E | validated | |
| MedDRA | 10047847 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
3
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:95409Acute adrenal insufficiency
rare endocrine diseases
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/100067
- This record as JSON: /data/d/100067.json