raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:100067

Waterhouse-Friderichsen syndrome

Type
Clinical subtype
Group
Subtype of disorder
Status
active

This disease is described under Acute adrenal insufficiency

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enWaterhouse-Friderichsen syndrome
frSyndrome de Waterhouse-Friderichsen
deWaterhouse-Friderichsen-Syndrom
esSíndrome de Waterhouse-Friderichsen
itSindrome di Waterhouse-Friderichsen
nlWaterhouse-Friderichsensyndroom
ptSíndrome de Waterhouse-Friedrickson
plZespół Waterhouse-Friderichsena
csWaterhouseův-Friderichsenův syndromWaterhouse-Friderichsenův syndrom
ukСиндром Уотерхауса-Фрідріхсена
zh华-弗综合征
trWaterhouse-Friderichsen sendromu
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10A39.1+Especificvalidated
ICD-10E35.1*NTBTinclusionvalidated
ICD-111C1C.1Especificvalidated
MONDO0006015Evalidated
MeSHD014884Evalidated
UMLSC1403891Evalidated
GARD9449Evalidated
MedDRA10047847Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card